{"id":"W4410946175","doi":"10.1111/pde.16001","title":"Blau Syndrome (Juvenile Systemic Granulomatosis): State‐Of‐The‐Art Review","year":2025,"lang":"en","type":"review","venue":"Pediatric Dermatology","topic":"Sarcoidosis and Beryllium Toxicity Research","field":"Medicine","cited_by":4,"is_retracted":false,"has_abstract":true,"ca_institutions":"SKiN Health; Quest University Canada; University of British Columbia","funders":"","keywords":"Medicine; Dermatology; Systemic therapy; Methotrexate; Uveitis; Thalidomide; Refractory (planetary science); Arthritis; Immunology; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0004938509,0.000823421,0.001682325,0.00359064,0.0002933015,0.001088768,0.0008032435,0.0008345776,0.005107522],"category_scores_gemma":[0.001146659,0.0002926546,0.0006147616,0.003415308,0.0003377013,0.001198053,0.0006208571,0.0009795635,0.001321757],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004062709,"about_ca_system_score_gemma":0.001336451,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001182794,"about_ca_topic_score_gemma":0.001960608,"domain_scores_codex":[0.9997965,0.00002945117,0.00005665795,0.0000381069,0.00006088275,0.00001851721],"domain_scores_gemma":[0.9993413,0.0003754351,0.0001356117,0.00001327661,0.00009583349,0.00003857678],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.00008613178,0.00005200426,0.000369905,0.05595647,0.0002074237,0.0006568333,0.00009359811,0.0002321483,0.0009218824,0.00124071,0.03193565,0.9082472],"study_design_scores_gemma":[0.00003060327,0.0001008419,0.001839206,0.02473617,0.0008050441,0.009198207,0.0001379195,0.00008096777,0.0003612323,0.001216506,0.9614593,0.00003387621],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.00009368415,0.9992402,0.00003596849,0.0001184775,0.00008509435,0.000002379691,0.00002118085,0.000005030211,0.0003980236],"genre_scores_gemma":[0.0006147883,0.9989103,0.00009367896,0.00009878987,0.00009437578,0.000003025635,0.00003852706,0.000001202189,0.0001453379],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.005107522,"threshold_uncertainty_score":0.01708639,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02563984815767962,"score_gpt":0.3423311932067037,"score_spread":0.3166913450490241,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}