{"id":"W4410946175","doi":"10.1111/pde.16001","title":"Blau Syndrome (Juvenile Systemic Granulomatosis): State‐Of‐The‐Art Review","year":2025,"lang":"en","type":"review","venue":"Pediatric Dermatology","topic":"Sarcoidosis and Beryllium Toxicity Research","field":"Medicine","cited_by":4,"is_retracted":false,"has_abstract":true,"ca_institutions":"SKiN Health; Quest University Canada; University of British Columbia","funders":"","keywords":"Medicine; Dermatology; Systemic therapy; Methotrexate; Uveitis; Thalidomide; Refractory (planetary science); Arthritis; Immunology; Internal medicine","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":["metaepi_narrow","insufficient_payload"],"consensus_categories":[],"category_scores_codex":[0.0005813777,0.0006473205,0.00613415,0.0007768193,0.0001151269,0.00001636495,0.0009234655,0.000539344,0.0002911073],"category_scores_gemma":[0.0006853237,0.0004184284,0.001795974,0.002656955,0.0001841443,0.00004779605,0.0004978738,0.001101723,0.0007995084],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001673875,"about_ca_system_score_gemma":0.002485664,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00001380647,"about_ca_topic_score_gemma":0.000003850117,"domain_scores_codex":[0.9945621,0.0008961734,0.002294247,0.0007130599,0.0007709913,0.0007633895],"domain_scores_gemma":[0.9960967,0.0009367454,0.0009903809,0.001481121,0.000261991,0.0002330182],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"systematic_review","study_design_gemma":"not_applicable","study_design_scores_codex":[0.000005718703,0.0001835804,0.001456264,0.7954723,0.0002655189,0.0004762581,0.000007342164,4.370287e-8,2.356584e-7,0.00002361663,0.1029592,0.09914995],"study_design_scores_gemma":[0.0004056245,0.0000582519,0.00006986928,0.1077828,0.007276756,0.03774735,0.000002123418,0.000001172449,0.000002896687,0.00001323679,0.8462831,0.0003568959],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.00009253866,0.9933532,0.000008947347,0.0006124445,0.0006954371,0.003379106,0.0001422866,0.00008339094,0.00163267],"genre_scores_gemma":[0.0001317205,0.9938037,0.00003268117,0.0003934256,0.0001172002,0.0005387542,0.0001269792,0.0000700986,0.004785405],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.7433239,"threshold_uncertainty_score":0.9999785,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02563984815767962,"score_gpt":0.3423311932067037,"score_spread":0.3166913450490241,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}