{"id":"W4410975984","doi":"10.1016/j.jcf.2025.03.531","title":"WS07.04Baseline variability in percent predicted forced expiratory volume in one second predicts short-term lung function response to elexacaftor/tezacaftor/ivacaftor in people with cystic fibrosis","year":2025,"lang":"en","type":"article","venue":"Journal of Cystic Fibrosis","topic":"Cystic Fibrosis Research Advances","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":false,"ca_institutions":"St. Paul's Hospital; University of British Columbia","funders":"","keywords":"Ivacaftor; Cystic fibrosis; Medicine; Lung function; Vital capacity; Pulmonary function testing; Term (time); Internal medicine; Lung; Lung volumes; Cardiology; Cystic fibrosis transmembrane conductance regulator","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0005440608,0.000330484,0.0004429954,0.000402627,0.000449986,0.0007813803,0.0003086298,0.0006414342,0.003747561],"category_scores_gemma":[0.001822574,0.0001978032,0.000823689,0.0005927198,0.0002028138,0.0005673006,0.0005292045,0.0009218191,0.0007260318],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002515458,"about_ca_system_score_gemma":0.0003255314,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.003415019,"about_ca_topic_score_gemma":0.004766983,"domain_scores_codex":[0.9994553,0.0001244206,0.00006662938,0.0001166963,0.0001112472,0.0001257047],"domain_scores_gemma":[0.9988637,0.0002011679,0.0004008692,0.0001006667,0.0001832374,0.0002502982],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.001193844,0.0001942087,0.9939305,0.00001382546,0.0002033431,0.00007818228,0.00003466318,0.000055436,0.0007176504,0.00003225383,0.0006893811,0.002856705],"study_design_scores_gemma":[0.00001917854,0.0002214237,0.9990845,0.000004005066,0.00004165251,0.00009092204,0.00006453237,0.0001238834,0.0001012204,0.00002859644,0.0002160532,0.000003998647],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9957247,0.0001637838,0.0001058321,0.0001752247,0.00005907123,0.00001379611,0.00229693,0.00001464038,0.00144604],"genre_scores_gemma":[0.9962295,0.00006671415,0.0001318228,0.0001040431,0.00004891681,0.00002302672,0.002161756,0.000006950872,0.0012273],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.003747561,"threshold_uncertainty_score":0.01253682,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.009438573599859845,"score_gpt":0.2741532254069091,"score_spread":0.2647146518070492,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}