{"id":"W4412195360","doi":"10.1002/ppul.71107","title":"Repeatability of Multiple Breath Washout in Pediatric Primary Ciliary Dyskinesia","year":2025,"lang":"en","type":"article","venue":"Pediatric Pulmonology","topic":"Cystic Fibrosis Research Advances","field":"Medicine","cited_by":3,"is_retracted":false,"has_abstract":true,"ca_institutions":"Institute for Clinical Evaluative Sciences; SickKids Foundation; Hospital for Sick Children; BC Children's Hospital; University of Toronto","funders":"National Center for Advancing Translational Sciences; National Heart, Lung, and Blood Institute; Rare Diseases Clinical Research Network","keywords":"Medicine; Primary ciliary dyskinesia; Spirometry; Repeatability; Intraclass correlation; Subclinical infection; Concordance; Outpatient clinic; Vital capacity; Mucociliary clearance; Pulmonary function testing; Lung volumes; Internal medicine; Lung; Lung function; Bronchiectasis; Asthma; Diffusing capacity","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0006167834,0.0002373708,0.0008083623,0.001146257,0.00004172557,0.0000063535,0.000305576,0.0002496468,0.00006375094],"category_scores_gemma":[0.003134228,0.0002191255,0.0001423264,0.001828238,0.0001651477,0.0001209332,0.0002851472,0.0005107361,0.00002948177],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002867629,"about_ca_system_score_gemma":0.0007985372,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0002503677,"about_ca_topic_score_gemma":0.00008456717,"domain_scores_codex":[0.9973609,0.0001760548,0.0008500965,0.0006594658,0.0003381704,0.0006152592],"domain_scores_gemma":[0.9975307,0.001147654,0.0001680893,0.0008119077,0.0002043672,0.0001373055],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.000789595,0.0005821641,0.9904208,0.001303877,0.00001626125,0.0001011335,0.00004263485,0.0000162867,0.0007166014,0.00006483917,0.0007444434,0.005201334],"study_design_scores_gemma":[0.002170404,0.0002312143,0.9953043,0.00001829037,0.0001402314,0.00003535068,0.00002940225,0.0002483562,0.000246096,0.0007166303,0.0007188078,0.0001408905],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9857893,0.007598575,0.000352518,0.0009805342,0.0002916357,0.0007973553,0.00003318908,0.00009039997,0.00406648],"genre_scores_gemma":[0.9928516,0.003035136,0.002903588,0.0001164203,0.0003150965,0.00009843725,0.00006384293,0.00001993971,0.0005959122],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.007062314,"threshold_uncertainty_score":0.8935678,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.009699003803710587,"score_gpt":0.2884031586023373,"score_spread":0.2787041547986267,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}