{"id":"W4412195360","doi":"10.1002/ppul.71107","title":"Repeatability of Multiple Breath Washout in Pediatric Primary Ciliary Dyskinesia","year":2025,"lang":"en","type":"article","venue":"Pediatric Pulmonology","topic":"Cystic Fibrosis Research Advances","field":"Medicine","cited_by":3,"is_retracted":false,"has_abstract":true,"ca_institutions":"Institute for Clinical Evaluative Sciences; SickKids Foundation; Hospital for Sick Children; BC Children's Hospital; University of Toronto","funders":"National Center for Advancing Translational Sciences; National Heart, Lung, and Blood Institute; Rare Diseases Clinical Research Network","keywords":"Medicine; Primary ciliary dyskinesia; Spirometry; Repeatability; Intraclass correlation; Subclinical infection; Concordance; Outpatient clinic; Vital capacity; Mucociliary clearance; Pulmonary function testing; Lung volumes; Internal medicine; Lung; Lung function; Bronchiectasis; Asthma; Diffusing capacity","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.008066031,0.0003891265,0.0005852797,0.0007442049,0.0004356474,0.0006000177,0.0006646392,0.0005256697,0.000539485],"category_scores_gemma":[0.0184077,0.0003090088,0.0005790966,0.0005915465,0.0003768591,0.0003636227,0.0006759862,0.0005002782,0.0002093159],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0008857471,"about_ca_system_score_gemma":0.0006075294,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.010364,"about_ca_topic_score_gemma":0.01752657,"domain_scores_codex":[0.992413,0.001941188,0.000818191,0.001634489,0.002804796,0.0003883897],"domain_scores_gemma":[0.983029,0.005351582,0.005878605,0.001198983,0.004118737,0.0004230586],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0001584103,0.00003081761,0.9917417,0.000044107,0.0001213547,0.00007097058,0.0004125962,0.0001403853,0.0007878284,0.0000191736,0.0001632078,0.006309564],"study_design_scores_gemma":[0.000003636087,0.0002064884,0.9983473,0.000009819654,0.00004036234,0.0002314533,0.00008700375,0.0002998447,0.000507698,0.00001038583,0.0002505724,0.000005520054],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9961244,0.0009445508,0.001481869,0.00003343412,0.00002670997,0.00005691225,0.0004219473,0.00003982682,0.000870158],"genre_scores_gemma":[0.9986337,0.00006893913,0.0008140029,0.00001709451,0.00000916724,0.00003641009,0.0003298023,0.000009390346,0.00008157506],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.010364,"threshold_uncertainty_score":0.04265773,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.009699003803710587,"score_gpt":0.2884031586023373,"score_spread":0.2787041547986267,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}