{"id":"W4412532658","doi":"10.1212/nxg.0000000000200248","title":"Executive Function Deficits in Genetic Frontotemporal Dementia","year":2025,"lang":"en","type":"article","venue":"Neurology Genetics","topic":"Amyotrophic Lateral Sclerosis Research","field":"Medicine","cited_by":1,"is_retracted":false,"has_abstract":true,"ca_institutions":"McGill University; Douglas Mental Health University Institute; Western University; Sunnybrook Health Science Centre; Montreal Neurological Institute and Hospital; Occupational Cancer Research Centre; Université Laval","funders":"Medical Research Council; UK Dementia Research Institute; EU Joint Programme – Neurodegenerative Disease Research; National Institute for Health and Care Research; Brain Research UK; University College London; NIHR Cambridge Biomedical Research Centre; Wellcome Trust","keywords":"Frontotemporal dementia; Neuroscience; Executive functions; Psychology; Function (biology); Dementia; Physical medicine and rehabilitation; Cognitive psychology; Medicine; Cognition; Genetics; Biology; Internal medicine; Disease","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0005273346,0.0007287581,0.0002751718,0.001096825,0.0002979292,0.0003375669,0.0001679218,0.0003379232,0.001325257],"category_scores_gemma":[0.001958581,0.000105648,0.000143364,0.0003419283,0.0003538922,0.0001935139,0.000261888,0.0002441732,0.000137449],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003905633,"about_ca_system_score_gemma":0.0002096799,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.003728486,"about_ca_topic_score_gemma":0.004677081,"domain_scores_codex":[0.9998772,0.00002986504,0.00001601039,0.00002691733,0.0000337914,0.00001627302],"domain_scores_gemma":[0.999543,0.0001548525,0.0001844731,0.00001972809,0.00004543348,0.00005270471],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.001381063,0.0003200987,0.9716039,0.00006576865,0.0001472618,0.003303976,0.0004824005,0.0003632859,0.003279546,0.0001459873,0.0003867536,0.01851991],"study_design_scores_gemma":[0.00002667086,0.0002309409,0.9963326,0.00001455156,0.00003926625,0.002455286,0.00009232214,0.0001803864,0.0002455651,0.0002627316,0.0001154975,0.000004172497],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9992346,0.0002376052,0.00003025891,0.0000248001,0.000002903541,0.000002886909,0.00007141505,0.000003376316,0.0003922084],"genre_scores_gemma":[0.9996245,0.00007972223,0.00005555153,0.00001714427,0.000004769527,0.000003158381,0.0001150361,8.091005e-7,0.00009921819],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.003728486,"threshold_uncertainty_score":0.007413566,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01959816830241734,"score_gpt":0.2879154646189674,"score_spread":0.26831729631655,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}