{"id":"W4412532658","doi":"10.1212/nxg.0000000000200248","title":"Executive Function Deficits in Genetic Frontotemporal Dementia","year":2025,"lang":"en","type":"article","venue":"Neurology Genetics","topic":"Amyotrophic Lateral Sclerosis Research","field":"Medicine","cited_by":1,"is_retracted":false,"has_abstract":true,"ca_institutions":"McGill University; Douglas Mental Health University Institute; Western University; Sunnybrook Health Science Centre; Montreal Neurological Institute and Hospital; Occupational Cancer Research Centre; Université Laval","funders":"Medical Research Council; UK Dementia Research Institute; EU Joint Programme – Neurodegenerative Disease Research; National Institute for Health and Care Research; Brain Research UK; University College London; NIHR Cambridge Biomedical Research Centre; Wellcome Trust","keywords":"Frontotemporal dementia; Neuroscience; Executive functions; Psychology; Function (biology); Dementia; Physical medicine and rehabilitation; Cognitive psychology; Medicine; Cognition; Genetics; Biology; Internal medicine; Disease","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.00009922373,0.0001333402,0.0002286793,0.0002219977,0.00004581363,0.000009935283,0.0001114227,0.000210696,0.0001208445],"category_scores_gemma":[0.00004705641,0.0001262122,0.00004939524,0.0003021602,0.0001098775,0.00001796547,0.0001173317,0.0003814928,0.00005677138],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00003690352,"about_ca_system_score_gemma":0.0001258879,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0000726845,"about_ca_topic_score_gemma":0.0001614033,"domain_scores_codex":[0.9986481,0.0001399192,0.0002813737,0.0003663701,0.0001859787,0.0003782611],"domain_scores_gemma":[0.9994676,0.00004416328,0.00003709386,0.0002979977,0.00007624509,0.00007697388],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0006607541,0.0001222018,0.9784523,0.00002627114,0.0000645823,0.00009370704,0.00004004225,0.0002820154,0.009721852,0.0001014443,0.002260412,0.008174386],"study_design_scores_gemma":[0.001476826,0.000790979,0.9883365,0.00001358484,0.00007583561,0.00001448252,0.000005671724,0.002062604,0.0002504064,0.0006769577,0.00622391,0.00007223424],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9898844,0.001864849,0.0009966653,0.002591943,0.0003282801,0.0004280558,0.000001774735,0.0000360264,0.003868057],"genre_scores_gemma":[0.9951007,0.0003064183,0.0006137998,0.003298318,0.00006180006,0.00003483148,0.000008405352,0.00001658797,0.0005590996],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.009884176,"threshold_uncertainty_score":0.5146782,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01959816830241734,"score_gpt":0.2879154646189674,"score_spread":0.26831729631655,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}