{"id":"W4412808050","doi":"10.1111/ene.70314","title":"The Two Faces of Pediatric <scp>SCA2</scp>","year":2025,"lang":"en","type":"article","venue":"European Journal of Neurology","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":1,"is_retracted":false,"has_abstract":true,"ca_institutions":"Montreal Neurological Institute and Hospital","funders":"","keywords":"Medicine; Neuroscience; Pediatrics","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.001039112,0.0004885487,0.0004495116,0.0009066893,0.001232617,0.00145185,0.0004671103,0.001342862,0.005516976],"category_scores_gemma":[0.002503744,0.0002153952,0.0002625998,0.0008894458,0.001706451,0.001740074,0.001304372,0.002109862,0.0009106984],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0005848834,"about_ca_system_score_gemma":0.0008546533,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001905911,"about_ca_topic_score_gemma":0.004105638,"domain_scores_codex":[0.9991374,0.0001911379,0.00004398579,0.000183829,0.0002413992,0.000202222],"domain_scores_gemma":[0.9986803,0.0003059448,0.0003839733,0.00009111175,0.0001794495,0.0003592226],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"case_report","study_design_scores_codex":[0.0003659177,0.0001108604,0.4518273,0.0002858906,0.0001373498,0.1450196,0.004603136,0.0005142208,0.004351666,0.01417429,0.1490242,0.2295855],"study_design_scores_gemma":[0.0000261371,0.0001651399,0.2266267,0.0003763317,0.00009252252,0.6349758,0.007239989,0.0004839399,0.001069578,0.0123005,0.1165665,0.00007688732],"study_design_candidate":"case_report","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.7953069,0.02842052,0.01072442,0.09744585,0.002504184,0.00006572212,0.001395376,0.0004634956,0.06367362],"genre_scores_gemma":[0.9620397,0.00935267,0.005448426,0.01256325,0.003371834,0.00005533307,0.0006938274,0.0001460205,0.006328973],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.005516976,"threshold_uncertainty_score":0.0184561,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02307318277222353,"score_gpt":0.2710601789548953,"score_spread":0.2479869961826718,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}