{"id":"W4413048462","doi":"10.1177/18796397251358017","title":"The role of oligodendroglial dysfunction in Huntington's disease","year":2025,"lang":"en","type":"review","venue":"Journal of Huntington s Disease","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":3,"is_retracted":false,"has_abstract":true,"ca_institutions":"BC Children's Hospital; University of British Columbia","funders":"National Key Research and Development Program of China; Vetenskapsrådet; National Natural Science Foundation of China; Hjärnfonden; Bundesministerium für Bildung und Forschung; BC Children's Hospital; Michael Smith Health Research BC; Knut och Alice Wallenbergs Stiftelse; Deutsche Forschungsgemeinschaft; Huntington Society of Canada; Children's Health Research Institute","keywords":"Huntington's disease; Oligodendrocyte; Neuroscience; White matter; Huntingtin; Biology; Myelin; Disease; Pathology; Medicine; Central nervous system","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003463421,0.0006316578,0.000861693,0.001782369,0.0002226803,0.0006894558,0.0005628529,0.0007973881,0.0017601],"category_scores_gemma":[0.0003407602,0.0001611016,0.000230959,0.001484592,0.0002825769,0.0007918552,0.0005798797,0.0009339895,0.001129269],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004960832,"about_ca_system_score_gemma":0.0009169403,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001146958,"about_ca_topic_score_gemma":0.002211769,"domain_scores_codex":[0.9999214,0.00001171278,0.0000133722,0.00001235673,0.00003195069,0.000009184596],"domain_scores_gemma":[0.9998943,0.00003970028,0.00001661838,0.000002997133,0.00002937732,0.00001711808],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"design_other","study_design_gemma":"not_applicable","study_design_scores_codex":[0.00006719804,0.00003397587,0.0001594422,0.01374436,0.00006676195,0.0003414307,0.00007444844,0.0003033766,0.00181341,0.002680549,0.02652222,0.9541929],"study_design_scores_gemma":[0.00001749048,0.00009880874,0.001344846,0.003997027,0.0001128713,0.002106659,0.00006701821,0.00008336519,0.000369125,0.002148514,0.9896381,0.00001610992],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"review","genre_gemma":"review","genre_scores_codex":[0.0001068385,0.998936,0.00005107766,0.0001383357,0.0001242375,0.00000186917,0.0000101589,0.000005064811,0.0006263521],"genre_scores_gemma":[0.0005903403,0.9987827,0.00007370132,0.0001059362,0.00009232983,0.000002748823,0.00001914379,6.956823e-7,0.000332391],"genre_candidate":"review","genre_consensus":"review","teacher_disagreement_score":0.001782369,"threshold_uncertainty_score":0.005888104,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.0218876444276856,"score_gpt":0.3013188633041183,"score_spread":0.2794312188764327,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}