{"id":"W4413420152","doi":"10.1182/bloodadvances.2025016485","title":"Diagnosis of von Willebrand disease","year":2025,"lang":"en","type":"article","venue":"Blood Advances","topic":"Platelet Disorders and Treatments","field":"Medicine","cited_by":2,"is_retracted":false,"has_abstract":true,"ca_institutions":"Queen's University","funders":"Pfizer","keywords":"Von Willebrand disease; Medicine; Von Willebrand factor; Intensive care medicine; Disease; Pediatrics; Immunology; Pathology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.00001481374,0.00006507407,0.0001788584,0.00004895878,0.00002521664,0.000002673454,0.00003002138,0.00001575459,0.00004406276],"category_scores_gemma":[0.00005262821,0.00004905429,0.00005391514,0.0001175286,0.0000359121,0.00005630811,0.00001182286,0.00002538401,0.000004438262],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000003843307,"about_ca_system_score_gemma":0.00003333561,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00000671353,"about_ca_topic_score_gemma":0.000006609012,"domain_scores_codex":[0.9996173,0.000005854215,0.0001004888,0.0001137692,0.00007642873,0.00008617943],"domain_scores_gemma":[0.999736,0.00004223346,0.00002872356,0.000117531,0.00002266933,0.00005285151],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0001546259,0.0008459559,0.9596435,0.0002192445,0.0001563315,0.0001504827,0.00001887572,0.000004137412,0.00009150063,0.0003518162,0.0003745007,0.03798903],"study_design_scores_gemma":[0.01129566,0.0003726206,0.8137339,0.001141308,0.001842011,0.0000111124,0.0001186855,0.00002058604,0.03918017,0.008583068,0.123489,0.0002119385],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9610397,0.03195882,0.000009088149,0.0007030252,0.00006935538,0.0001647632,0.0000192921,0.00002015705,0.006015765],"genre_scores_gemma":[0.9944254,0.004100784,0.0002313769,0.0001885188,0.00001181003,0.00003937634,0.0000140186,0.000003957429,0.0009847477],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.1459096,"threshold_uncertainty_score":0.2000376,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.005399719638762212,"score_gpt":0.2682767507300469,"score_spread":0.2628770310912846,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}