{"id":"W4414105231","doi":"10.1016/j.cjca.2025.09.006","title":"Clinical Trajectory and Prognosis in Patients with LMNA-related Advanced Heart Failure Complicated by Muscle Dystrophy","year":2025,"lang":"en","type":"letter","venue":"Canadian Journal of Cardiology","topic":"Cardiomyopathy and Myosin Studies","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":false,"ca_institutions":"","funders":"University of Tokyo","keywords":"Heart failure; Cardiomyopathy; Heart transplantation; Muscular dystrophy; Dilated cardiomyopathy; Lamin; Dystrophy","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":true,"about_ca":false,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003128081,0.00024779,0.0005472357,0.0006779323,0.001338935,0.0006922567,0.0004118191,0.001964335,0.001781852],"category_scores_gemma":[0.003138433,0.0001900518,0.0003492767,0.001005659,0.0004418759,0.0007342139,0.000450941,0.001661526,0.0003802956],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0007226655,"about_ca_system_score_gemma":0.0007759006,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.005923888,"about_ca_topic_score_gemma":0.007866913,"domain_scores_codex":[0.9997199,0.00005194031,0.00003643356,0.00003975094,0.00004256477,0.0001093458],"domain_scores_gemma":[0.9988551,0.0002531038,0.0001581038,0.00003866893,0.0001472503,0.0005476774],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0002468691,0.00009340035,0.9485159,0.00001727912,0.00002084145,0.04537261,0.000279542,0.0001230823,0.0003138236,0.0002082197,0.002041805,0.00276664],"study_design_scores_gemma":[0.00003836099,0.0002685555,0.9183223,0.0001046523,0.00004145515,0.07560346,0.001637121,0.001300526,0.00007554949,0.001111617,0.001459699,0.0000367279],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9771563,0.001317278,0.000171636,0.01279042,0.0002540162,0.00002233423,0.0002702078,0.00001400325,0.008003821],"genre_scores_gemma":[0.9964169,0.0004981234,0.0001418832,0.00172138,0.0005498012,0.00001190336,0.0001735829,0.000003840698,0.0004825112],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.005923888,"threshold_uncertainty_score":0.01177883,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.008451949243962191,"score_gpt":0.2374484084679904,"score_spread":0.2289964592240282,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}