{"id":"W4415027969","doi":"10.21203/rs.3.rs-7593592/v1","title":"VEXAS syndrome, immunodeficiency, and risk of infection","year":2025,"lang":"en","type":"preprint","venue":"Research Square","topic":"Otitis Media and Relapsing Polychondritis","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":false,"ca_institutions":"University of Alberta","funders":"","keywords":"Pneumonia; Mononucleosis; Immunodeficiency Syndrome; Retrospective cohort study; Immunodeficiency; Bone marrow; Tocilizumab; Viral disease","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0009441358,0.0001773647,0.0005229182,0.0008746411,0.0001600466,0.00003847037,0.0001086169,0.0005000309,0.00009937365],"category_scores_gemma":[0.001156208,0.0001554819,0.0001722385,0.0004933202,0.0004478621,0.00003080357,0.0006416106,0.002278176,0.00002216975],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001401272,"about_ca_system_score_gemma":0.0005414402,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.004153229,"about_ca_topic_score_gemma":0.00009592355,"domain_scores_codex":[0.9975978,0.0003683191,0.0003482196,0.000455196,0.0008384273,0.0003920545],"domain_scores_gemma":[0.9982661,0.0003410435,0.0001126914,0.0006400995,0.0004936548,0.0001464002],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0002886669,0.0009751305,0.9160897,0.02230635,0.0008040747,0.0006904529,0.001615196,0.00005452522,0.001239716,0.0007009624,0.01435858,0.04087668],"study_design_scores_gemma":[0.002117151,0.001824104,0.9484454,0.02087693,0.0004612073,0.0006397232,0.0002627911,0.0004418557,0.00267776,0.002239826,0.01964284,0.0003703972],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9717131,0.01335695,0.00007270664,0.0002868901,0.003471544,0.0009753011,0.0001843683,0.00006255207,0.009876624],"genre_scores_gemma":[0.9300521,0.04910119,0.0003007492,0.000006955316,0.00008534682,0.00006625338,0.00009210651,0.00002260101,0.02027272],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.04166098,"threshold_uncertainty_score":0.9897668,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.03213061403199573,"score_gpt":0.3863408274475416,"score_spread":0.3542102134155459,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}