{"id":"W4415119457","doi":"10.1017/cjn.2025.10452","title":"Mortality in Children with Optic Nerve Hypoplasia/Septo-Optic-Pituitary Dysplasia","year":2025,"lang":"en","type":"article","venue":"Canadian Journal of Neurological Sciences / Journal Canadien des Sciences Neurologiques","topic":"Growth Hormone and Insulin-like Growth Factors","field":"Medicine","cited_by":2,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of Manitoba","funders":"","keywords":"Dysplasia; Optic nerve; Disease; Comorbidity; Mortality rate; Incidence (geometry); Lifetime risk; Epidemiology","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":true,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0004167268,0.0002957777,0.0001891746,0.001096433,0.0003009306,0.0003374249,0.0003038447,0.0002188432,0.0006942691],"category_scores_gemma":[0.001055009,0.000175638,0.0002463319,0.0008502286,0.0003032208,0.0001742186,0.0002923147,0.0002859448,0.00009507551],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.001346221,"about_ca_system_score_gemma":0.0009496816,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.1132915,"about_ca_topic_score_gemma":0.1409855,"domain_scores_codex":[0.9997509,0.00004245331,0.00001799259,0.00005672068,0.00007411202,0.0000577354],"domain_scores_gemma":[0.9994797,0.00004765111,0.0003031387,0.00001845784,0.00007737851,0.00007374121],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0000131688,0.000002414122,0.9995525,0.000004219283,0.000008096848,0.00003001704,0.00002328245,0.00002008821,0.0000407647,0.000004497734,0.0000338008,0.000267074],"study_design_scores_gemma":[0.000001257085,0.00001399729,0.9995815,0.000005379477,0.000007187828,0.0001580543,0.00006934411,0.00004589555,0.00003608262,0.000005054694,0.00007528732,8.628886e-7],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9985731,0.0003672749,0.00005555743,0.00003255521,0.000003314935,0.000004611694,0.0007496967,0.000004440771,0.0002093714],"genre_scores_gemma":[0.9986836,0.0002822384,0.00009599327,0.00001172828,0.00000435179,0.000006064323,0.0008080357,0.000001306879,0.0001065448],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.1132915,"threshold_uncertainty_score":0.2252642,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02152775135996021,"score_gpt":0.2625768137223053,"score_spread":0.2410490623623451,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}