{"id":"W4415484294","doi":"10.1212/nxg.0000000000200313","title":"Developing a National Network for Leukodystrophy Research and Care in Canada","year":2025,"lang":"en","type":"article","venue":"Neurology Genetics","topic":"Neutrophil, Myeloperoxidase and Oxidative Mechanisms","field":"Immunology and Microbiology","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"Montreal Children's Hospital; Oakville-Trafalgar Memorial Hospital; Child and Family Research Institute; London Health Sciences Centre; Western University; McGill University; McGill University Health Centre; Children's Hospital of Western Ontario; Montreal Neurological Institute and Hospital","funders":"","keywords":"Excellence; Leukodystrophy; White paper; Multidisciplinary approach; Center of excellence; Disease; Translational research","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"codex-gemma-dda1882f352a","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001867625,0.000108817,0.0001779892,0.0001415588,0.0002154743,0.000007224085,0.0001623003,0.0001515999,0.00001041236],"category_scores_gemma":[0.00005797539,0.0001112345,0.00001480285,0.0002382547,0.0001267135,0.00001238562,0.0001379882,0.0003415681,0.00000453785],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001488185,"about_ca_system_score_gemma":0.001725435,"about_ca_topic_candidate":true,"about_ca_topic_consensus":true,"about_ca_topic_score_codex":0.01717764,"about_ca_topic_score_gemma":0.4582243,"domain_scores_codex":[0.9988077,0.0002007588,0.0001917255,0.0003209489,0.00004070775,0.0004382121],"domain_scores_gemma":[0.9992028,0.00038488,0.00002790181,0.0001125161,0.0002588942,0.00001303751],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"theoretical_or_conceptual","study_design_gemma":"not_applicable","study_design_scores_codex":[0.003328631,0.0001281308,0.1771047,0.0003960767,0.0004428472,0.000155437,0.0008901791,0.002992362,0.3261937,0.405066,0.04365623,0.03964569],"study_design_scores_gemma":[0.006170446,0.0019093,0.1594197,0.00008588406,0.00003466365,0.00007284213,0.0007231917,0.000132829,0.1926122,0.06024304,0.5780101,0.0005857337],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9916195,0.004401767,0.0004388672,0.001993055,0.0006831131,0.0003812083,0.00003319635,0.000009406035,0.0004398981],"genre_scores_gemma":[0.9964917,0.0001699376,0.0008433352,0.002108285,0.00004219696,0.00008817264,0.00005133295,0.00001025655,0.0001948143],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.5343539,"threshold_uncertainty_score":0.9893671,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.04352204077441683,"score_gpt":0.3053174441484925,"score_spread":0.2617954033740756,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}