{"id":"W4415799849","doi":"10.1161/circ.152.suppl_3.4367364","title":"Abstract 4367364: A Multicenter Friedreich Ataxia Registry Identifies Posterior Wall Thickness as a Predictor of Major Adverse Cardiac Events","year":2025,"lang":"en","type":"article","venue":"Circulation","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"Hospital for Sick Children; University of Toronto; SickKids Foundation; Centre Hospitalier Universitaire Sainte-Justine","funders":"","keywords":"Mace; Logistic regression; Univariate analysis; Ataxia; Heart failure; Sudden cardiac death; Heart disease","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.002052731,0.0003107882,0.0005214837,0.00138085,0.0004444846,0.0007026918,0.0005219342,0.0004576258,0.001456331],"category_scores_gemma":[0.002484601,0.0002613654,0.0002489611,0.001687607,0.0002104,0.0005819535,0.0006557035,0.0003584206,0.0005992334],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002863166,"about_ca_system_score_gemma":0.0006922398,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.003552072,"about_ca_topic_score_gemma":0.004576511,"domain_scores_codex":[0.9989725,0.0003123604,0.0001733976,0.0002533057,0.0002020244,0.00008639417],"domain_scores_gemma":[0.9962651,0.0005078861,0.001567396,0.0004704333,0.0005433952,0.0006458241],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0002721525,0.00004304936,0.9961966,0.00001514653,0.00005241367,0.00009529435,0.00004603008,0.00006010398,0.0006440321,0.00001581261,0.001091265,0.001468064],"study_design_scores_gemma":[0.00004197069,0.0001080289,0.9986857,0.00000852079,0.00004534142,0.0002363614,0.00003619963,0.000190548,0.0001596356,0.000009232275,0.0004749199,0.000003669209],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9891912,0.0001800915,0.0003075193,0.0001005849,0.00001002054,0.00007461409,0.009203538,0.0000448794,0.0008875862],"genre_scores_gemma":[0.9830374,0.000110771,0.0007614416,0.00006229614,0.00005026943,0.0001399076,0.01541786,0.00001605036,0.0004039349],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.003552072,"threshold_uncertainty_score":0.01085597,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01772690495698751,"score_gpt":0.2781797641849278,"score_spread":0.2604528592279403,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}