{"id":"W4416139243","doi":"10.1002/ppul.71372","title":"New Treatments Are Urgently Needed for Patients With All Primary Ciliary Dyskinesia Genotypes","year":2025,"lang":"en","type":"article","venue":"Pediatric Pulmonology","topic":"Cystic Fibrosis Research Advances","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"McGill University","funders":"","keywords":"Primary ciliary dyskinesia; Respiratory distress; Disease; Bronchiectasis; Lung; Dyskinesia; Respiratory disease; Lung function","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.004339894,0.000914094,0.002358691,0.0007840706,0.002113817,0.003041851,0.002454229,0.02179526,0.005334115],"category_scores_gemma":[0.0245982,0.0005171736,0.00211179,0.0004410034,0.002418423,0.007763169,0.001528063,0.03174414,0.003959007],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0020412,"about_ca_system_score_gemma":0.002705403,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.002145124,"about_ca_topic_score_gemma":0.004047891,"domain_scores_codex":[0.9965759,0.001220728,0.0005156332,0.0004034527,0.0009022802,0.0003820158],"domain_scores_gemma":[0.9781209,0.01085947,0.001654495,0.0005582289,0.005868263,0.002938686],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"not_applicable","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0001269784,0.00004208014,0.001382347,0.0003841585,0.00005375915,0.001561027,0.0001784465,0.00005828476,0.0002552055,0.001002879,0.9561961,0.03875887],"study_design_scores_gemma":[0.0001391555,0.0001554831,0.002504179,0.00132885,0.0001406854,0.007431398,0.001025156,0.0003386134,0.000435814,0.008285352,0.9780605,0.0001546717],"study_design_candidate":"not_applicable","study_design_consensus":"not_applicable","genre_codex":"commentary","genre_gemma":"commentary","genre_scores_codex":[0.0004746976,0.0190626,0.0003614789,0.9340419,0.04517235,0.00001299425,0.00008382404,0.00008051574,0.0007096737],"genre_scores_gemma":[0.005196791,0.01441202,0.001149071,0.8558383,0.1208884,0.00005524768,0.00007771209,0.00005937808,0.002322987],"genre_candidate":"commentary","genre_consensus":"commentary","teacher_disagreement_score":0.02179526,"threshold_uncertainty_score":0.02295178,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.008024647805744021,"score_gpt":0.2701736612375514,"score_spread":0.2621490134318074,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}