{"id":"W4416591177","doi":"10.1001/jamanetworkopen.2025.45294","title":"Condition-Specific Growth Charts for Children With Alagille Syndrome","year":2025,"lang":"en","type":"article","venue":"JAMA Network Open","topic":"Pediatric Hepatobiliary Diseases and Treatments","field":"Medicine","cited_by":1,"is_retracted":false,"has_abstract":true,"ca_institutions":"Children's Hospital of Eastern Ontario; University of Manitoba; London Health Sciences Centre; Western University; Children's Hospital of Western Ontario; University of Toronto; University Health Network; Toronto General Hospital; Institute of Health Services and Policy Research; Hospital for Sick Children","funders":"Grifols; Ipsen; Hospital for Sick Children; National Natural Science Foundation of China; Sarepta Therapeutics; CSL Behring; National Institute of Diabetes and Digestive and Kidney Diseases; Fudan University; Alnylam Pharmaceuticals; Gilead Sciences","keywords":"Alagille syndrome; Growth chart; MEDLINE; Growth retardation; Congenital disease","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.008307725,0.0008424546,0.0005950182,0.00803359,0.0004138114,0.001041855,0.0009194008,0.0003830492,0.002306981],"category_scores_gemma":[0.03276282,0.0002148851,0.0008403731,0.005741464,0.0004498293,0.0008234406,0.001339483,0.0007067951,0.0003705404],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.00117233,"about_ca_system_score_gemma":0.002243394,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.01331156,"about_ca_topic_score_gemma":0.01671342,"domain_scores_codex":[0.9950505,0.00206344,0.0009741487,0.0004427729,0.001285702,0.0001834798],"domain_scores_gemma":[0.9804457,0.005897964,0.008610186,0.001493721,0.003164875,0.0003876702],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.000247249,0.00004775447,0.9378147,0.0001860129,0.0001271931,0.0002140805,0.0004728009,0.005061857,0.0003160295,0.001286334,0.01019009,0.04403592],"study_design_scores_gemma":[0.00006474186,0.0002662037,0.9614139,0.0002927811,0.00010301,0.001082845,0.001176862,0.01447218,0.001112619,0.001354612,0.01858018,0.00008020205],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.784125,0.002691941,0.08827026,0.001308302,0.0003272957,0.001661708,0.1060796,0.003060386,0.0124755],"genre_scores_gemma":[0.8445755,0.001318627,0.1000909,0.0001343845,0.00008471461,0.002202162,0.0502316,0.0002821562,0.001079959],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.01331156,"threshold_uncertainty_score":0.04393595,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01098869438992312,"score_gpt":0.2743648620154979,"score_spread":0.2633761676255748,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}