{"id":"W4417151606","doi":"10.1136/thorax-2025-223687","title":"Heterogeneity of short-term elexacaftor-tezacaftor-ivacaftor response in cystic fibrosis using <sup>129</sup> Xe MRI","year":2025,"lang":"en","type":"article","venue":"Thorax","topic":"Cystic Fibrosis Research Advances","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"BC Children's Hospital; University of British Columbia","funders":"Reseau canadien de recherche respiratoire; Michael Smith Health Research BC; Vertex Pharmaceuticals","keywords":"Cystic fibrosis; Lung disease; Lung; Disease; Respiratory disease; Pancreatic disease","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.00245157,0.0001430798,0.0003746029,0.0005540945,0.0001060148,0.0004223824,0.0002448017,0.0003621878,0.0008081394],"category_scores_gemma":[0.005973856,0.00008263889,0.0003368529,0.0003557976,0.000280478,0.0003869049,0.0003627064,0.0002198217,0.0001135789],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0001985568,"about_ca_system_score_gemma":0.0000888107,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0007481474,"about_ca_topic_score_gemma":0.000789656,"domain_scores_codex":[0.9988396,0.0005246602,0.0001366617,0.0002355241,0.0001616012,0.0001019812],"domain_scores_gemma":[0.9933448,0.003326833,0.002441764,0.0004027245,0.0002382305,0.0002456538],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.002354869,0.00004024645,0.9818996,0.0000314056,0.0003893485,0.0001323011,0.000164235,0.000287687,0.004559988,0.00002562649,0.000111079,0.01000355],"study_design_scores_gemma":[0.00001145892,0.0004028162,0.9985304,0.000003594936,0.00004771666,0.0002165401,0.00005840299,0.0002988741,0.0003283162,0.00002305823,0.00007558479,0.000003227315],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9993497,0.0003195044,0.0001005667,0.00002077307,0.000001648052,0.000003441269,0.00008424713,0.000002857138,0.0001173945],"genre_scores_gemma":[0.9998636,0.0000194061,0.00001834566,0.000006591695,0.000002594163,0.00000154649,0.00006449413,7.194599e-7,0.00002262694],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.00245157,"threshold_uncertainty_score":0.01296526,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02983122851737804,"score_gpt":0.365928512223949,"score_spread":0.3360972837065709,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}