{"id":"W4417531214","doi":"10.1093/eurheartj/ehaf965","title":"Catecholaminergic polymorphic ventricular tachycardia mediated by ryanodine receptor 2: a validated risk stratification","year":2025,"lang":"en","type":"article","venue":"European Heart Journal","topic":"Cardiac electrophysiology and arrhythmias","field":"Medicine","cited_by":2,"is_retracted":false,"has_abstract":true,"ca_institutions":"Western University; Population Health Research Institute; London Health Sciences Centre; BC Children's Hospital; University of British Columbia","funders":"Nederlandse Federatie van Universitair Medische Centra; Umeå Universitet; Hjärt-Lungfonden; Great Ormond Street Hospital for Children; National Health and Medical Research Council; Novo Nordisk Fonden; Norges Forskningsråd; Ministerstvo Zdravotnictví Ceské Republiky; Asociación Española de Psicología Conductual; Instituto de Salud Carlos III; ZonMw; Agence Nationale de la Recherche; E-Rare; Deutsches Zentrum für Herz-Kreislaufforschung; Medical Research Council; Koninklijke Nederlandse Akademie van Wetenschappen; Japan Agency for Medical Research and Development; Canadian Institutes of Health Research; Hartstichting; Heart and Stroke Foundation of Canada","keywords":"Catecholaminergic polymorphic ventricular tachycardia; Risk stratification; Ryanodine receptor; Ventricular tachycardia; Risk assessment; Tachycardia","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.007680161,0.0008766389,0.0006479316,0.000690735,0.0002454282,0.0009463383,0.0007758907,0.0006044751,0.0007745104],"category_scores_gemma":[0.01371483,0.0002563332,0.001018025,0.0003398847,0.0002913809,0.0003339432,0.0007552811,0.001053652,0.0003232759],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0004785989,"about_ca_system_score_gemma":0.0009660048,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.002820207,"about_ca_topic_score_gemma":0.002371097,"domain_scores_codex":[0.9985883,0.0007387882,0.00007941828,0.0003388011,0.0001667533,0.00008789964],"domain_scores_gemma":[0.9940442,0.003687937,0.000861961,0.0006140019,0.0006231936,0.0001686864],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.001800428,0.0003629902,0.8904306,0.0000749859,0.001365292,0.00032767,0.000123238,0.06533654,0.001269493,0.0004384989,0.001774086,0.03669622],"study_design_scores_gemma":[0.0004485688,0.001035625,0.2841712,0.0000892068,0.0008112733,0.0006864473,0.00006337122,0.7089691,0.001058905,0.001647121,0.0009636706,0.0000553802],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9702429,0.0004874814,0.02657835,0.0003546977,0.00003850738,0.0001534443,0.001200946,0.000140505,0.0008031158],"genre_scores_gemma":[0.992946,0.00009544769,0.005413083,0.00004861703,0.00001999613,0.00004388925,0.001250453,0.000008632923,0.0001739058],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.007680161,"threshold_uncertainty_score":0.04061705,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01116408829554884,"score_gpt":0.2628717723372422,"score_spread":0.2517076840416934,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}