{"id":"W50439370","doi":"10.1017/s0317167100052811","title":"Biogenic Amine Metabolites and Thiamine in Cerebrospinal Fluid in Heredo-Degenerative Ataxias","year":2001,"lang":"en","type":"article","venue":"Canadian Journal of Neurological Sciences / Journal Canadien des Sciences Neurologiques","topic":"Genetic Neurodegenerative Diseases","field":"Neuroscience","cited_by":24,"is_retracted":false,"has_abstract":true,"ca_institutions":"Université de Montréal; McGill University; Hôtel-Dieu de Montréal; Hotel Dieu Hospital","funders":"Medical Research Council; Medical Research Council Canada","keywords":"Homovanillic acid; Olivopontocerebellar atrophy; Cerebrospinal fluid; Thiamine; Internal medicine; Endocrinology; Ataxia; Metabolite; Serotonin; Biogenic amine; Neurochemical; Medicine; Central nervous system disease; Degenerative disease; Psychiatry","routes":{"ca_aff":true,"ca_fund":true,"ca_venue":true,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0001435964,0.0003696543,0.0002399974,0.001061569,0.0002964906,0.0003372403,0.0001237901,0.0002906301,0.0007927785],"category_scores_gemma":[0.0005371013,0.0001198806,0.0001143157,0.0004277276,0.0002849184,0.0001759646,0.0001854818,0.0001683045,0.0001341494],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002441301,"about_ca_system_score_gemma":0.0001317874,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001960675,"about_ca_topic_score_gemma":0.001663216,"domain_scores_codex":[0.9999168,0.0000161297,0.00001449239,0.00002227739,0.00001668724,0.00001360969],"domain_scores_gemma":[0.9997527,0.00005353704,0.00009407044,0.000008873545,0.00003892563,0.00005191131],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.001179651,0.00009347084,0.9518142,0.00008478625,0.0001089505,0.001465169,0.0003879377,0.00009463065,0.03724208,0.00002246147,0.00006568484,0.007440906],"study_design_scores_gemma":[0.00002231791,0.0005408628,0.9885931,0.00001320863,0.00007103597,0.003720275,0.0002817099,0.0001433805,0.006267642,0.0000335316,0.0003066699,0.000006228829],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9993449,0.0004699768,0.00003916862,0.000005615401,0.00000154971,0.000001669104,0.00005317491,0.000003448181,0.00008057591],"genre_scores_gemma":[0.9995188,0.000167801,0.0001504443,0.000008466118,0.00000315896,0.000003057275,0.0000864781,0.000001099867,0.00006078191],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001960675,"threshold_uncertainty_score":0.003898561,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.04385699583825772,"score_gpt":0.2766517334989915,"score_spread":0.2327947376607338,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}