{"id":"W6958118099","doi":"10.60692/0m9s6-sgj69","title":"Rapid progression and mortality of lysosomal acid lipase deficiency presenting in infants","year":2016,"lang":"en","type":"article","venue":"Greater South Information System","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"SickKids Foundation; Hospital for Sick Children; University of Alberta","funders":"","keywords":"Confidence interval; Population; Medical record; Survival analysis; Cause of death; Young adult","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0008093316,0.0001865192,0.0002320665,0.0005714276,0.0002100599,0.0003923325,0.0001759064,0.00027414,0.0006716397],"category_scores_gemma":[0.003167689,0.0001333287,0.0002521504,0.000316519,0.0001956238,0.0003386806,0.0004555195,0.0005089479,0.0001462113],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0002402392,"about_ca_system_score_gemma":0.0002368147,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0008773495,"about_ca_topic_score_gemma":0.0008175763,"domain_scores_codex":[0.999559,0.000176258,0.00004651945,0.00007455471,0.00008256948,0.00006116162],"domain_scores_gemma":[0.99804,0.0005136599,0.0009944029,0.0001140214,0.0001243857,0.0002135543],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0002372468,0.00001262473,0.9935032,0.000009519322,0.00002285841,0.0005649271,0.0001142859,0.0001402175,0.0004253867,0.00005733603,0.0001180775,0.004794396],"study_design_scores_gemma":[0.00000908531,0.0002312863,0.9946127,0.00001656338,0.00002634159,0.003640389,0.0001301992,0.0005595688,0.0003951167,0.0001149131,0.0002571982,0.000006694853],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9988958,0.000527793,0.0001588811,0.00003887825,0.000003603049,0.000002978732,0.0001257466,0.000006482211,0.0002399629],"genre_scores_gemma":[0.9993719,0.0002457811,0.00009116651,0.00001022304,0.0000101981,0.000003268988,0.0002026415,0.000002292802,0.00006240181],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.0008773495,"threshold_uncertainty_score":0.00428021,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.04602594042468788,"score_gpt":0.2916896966168336,"score_spread":0.2456637561921458,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}