{"id":"W6962986546","doi":"10.18131/wes0z-3jh68","title":"Juvenile GM2 Gangliosidoses","year":2006,"lang":"en","type":"article","venue":"Galter Health Sciences Library, Northwestern University","topic":"Lysosomal Storage Disorders Research","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"","keywords":"Gangliosidosis; Juvenile; Natural history; Natural history study","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002852516,0.0004427396,0.0002311335,0.001849501,0.0006872008,0.0003709634,0.0002357114,0.0002137271,0.001156576],"category_scores_gemma":[0.001485932,0.0003295728,0.0002112785,0.001063078,0.0007147381,0.000273935,0.0003770972,0.0001581018,0.0001759807],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000527501,"about_ca_system_score_gemma":0.0003616861,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.003159106,"about_ca_topic_score_gemma":0.006665344,"domain_scores_codex":[0.9996402,0.00004979566,0.00006162928,0.00008877858,0.00008795515,0.0000716525],"domain_scores_gemma":[0.999203,0.0002028033,0.0002790527,0.00008532286,0.00007732323,0.0001524794],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"not_applicable","study_design_scores_codex":[0.0002131032,0.00007685241,0.8852412,0.00007124123,0.0000644102,0.08956319,0.001852487,0.0001096443,0.01340741,0.0001821915,0.0002429108,0.008975456],"study_design_scores_gemma":[0.00002315977,0.000128303,0.7133346,0.00002867756,0.00008139266,0.2812839,0.0007145076,0.0001694008,0.002504518,0.0001283998,0.001586378,0.00001684345],"study_design_candidate":"not_applicable","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"review","genre_scores_codex":[0.9992942,0.0002190595,0.00008354893,0.000009632334,0.000001785507,0.000006461184,0.00004536152,0.000003551386,0.0003363834],"genre_scores_gemma":[0.9993719,0.0001955214,0.0001374242,0.00001191941,0.000006727144,0.000005433373,0.000116011,0.000002681667,0.0001524773],"genre_candidate":"review","genre_consensus":null,"teacher_disagreement_score":0.003159106,"threshold_uncertainty_score":0.006281435,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02140180872912413,"score_gpt":0.2707181521801774,"score_spread":0.2493163434510532,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}