{"id":"W7039641331","doi":"","title":"Mucopolysaccharidosis type IIIC : molecular defects and pathophysiological mechanism","year":2021,"lang":"fr","type":"dissertation","venue":"Papyrus : Institutional Repository (Université de Montréal)","topic":"Power Systems Fault Detection","field":"Engineering","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"","keywords":"Lysosomal storage disease; Animal model; Pathophysiology; Mucopolysaccharidosis","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002817728,0.0006592821,0.0003753436,0.0004413082,0.0002531665,0.0006220926,0.0003267702,0.0007892193,0.001016597],"category_scores_gemma":[0.0001214617,0.0001682506,0.0003194383,0.0001871391,0.0008127309,0.0004712348,0.0003628226,0.0004962322,0.0002759316],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0006638697,"about_ca_system_score_gemma":0.0005164987,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.00148974,"about_ca_topic_score_gemma":0.000676949,"domain_scores_codex":[0.9999017,0.00001661146,0.00001610329,0.00002288307,0.00002235266,0.00002034779],"domain_scores_gemma":[0.9999074,0.00001234819,0.0000361987,0.00000749713,0.0000102324,0.00002626909],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.0006925451,0.000166845,0.008533851,0.001256361,0.00008242406,0.00851036,0.0002381351,0.0008871872,0.9401389,0.016252,0.001155513,0.02208594],"study_design_scores_gemma":[0.0003164225,0.003094039,0.1960687,0.001217127,0.0004933646,0.0687186,0.002110851,0.004155267,0.603198,0.01412657,0.1062986,0.0002024492],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.873614,0.1021628,0.008270237,0.003365494,0.0002932294,0.000148613,0.0009090547,0.0002962571,0.01094032],"genre_scores_gemma":[0.939092,0.04979797,0.00500394,0.0005532387,0.0001350499,0.0001659004,0.0006555683,0.00002018079,0.004576224],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.00148974,"threshold_uncertainty_score":0.004816771,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.003886748543896567,"score_gpt":0.1631981483231804,"score_spread":0.1593113997792838,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}