{"id":"W7057901514","doi":"","title":"Long-term intravenous treatment of Pompe disease with recombinant human alfa-glucosidase from milk","year":2004,"lang":"","type":"article","venue":"EUR Research Repository (Erasmus University Rotterdam)","topic":"Magnetic confinement fusion research","field":"Physics and Astronomy","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"Fondation pour la Recherche Médicale","keywords":"Disease; Recombinant DNA; Antibody; Clinical trial","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0003806005,0.0003772973,0.0008419806,0.0001182017,0.000294605,0.0003021003,0.0002897318,0.0003866096,0.0006787427],"category_scores_gemma":[0.0004153251,0.0001172413,0.0002508307,0.0001095836,0.0004386594,0.0003116374,0.0002136538,0.0008488598,0.0002015284],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.000279984,"about_ca_system_score_gemma":0.0002534394,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0001574818,"about_ca_topic_score_gemma":0.0002300566,"domain_scores_codex":[0.9998603,0.00004912178,0.000009925423,0.00002374953,0.00001841161,0.00003863232],"domain_scores_gemma":[0.9998183,0.00004557437,0.00003781348,0.00001826683,0.000008961195,0.00007115993],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"observational","study_design_scores_codex":[0.1639115,0.02649871,0.06605338,0.0008756822,0.0005681359,0.003763528,0.0004448351,0.001693085,0.5191163,0.0003421958,0.00198236,0.2147501],"study_design_scores_gemma":[0.02933632,0.7350506,0.1208295,0.0001313921,0.0004324274,0.008368462,0.0002134804,0.002531507,0.09473362,0.000152946,0.008173255,0.00004658038],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9978393,0.001450097,0.0002638813,0.00005184992,0.0000157913,0.00005692938,0.00003986972,0.00002027689,0.000261821],"genre_scores_gemma":[0.9988028,0.0003632007,0.000329056,0.00008237956,0.00003064615,0.00006070432,0.0001508026,0.00000310776,0.0001773647],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.0008419806,"threshold_uncertainty_score":0.002270639,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.02575140409415933,"score_gpt":0.2721303342034961,"score_spread":0.2463789301093368,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}