{"id":"W7095555207","doi":"","title":"Defects in energy homeostasis in Leigh syndrome French Canadian variant","year":2006,"lang":"en","type":"article","venue":"","topic":"Mitochondrial Function and Pathology","field":"Biochemistry, Genetics and Molecular Biology","cited_by":0,"is_retracted":false,"has_abstract":false,"ca_institutions":"","funders":"","keywords":"Energy homeostasis; Energy metabolism; Disease; Energy (signal processing)","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0004684399,0.001273925,0.0006976503,0.002082186,0.002357706,0.000715137,0.001264945,0.00109781,0.01026975],"category_scores_gemma":[0.001639939,0.0002852461,0.0006433459,0.001604893,0.001325866,0.0003483582,0.0005913799,0.0005990746,0.0006785506],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.004028278,"about_ca_system_score_gemma":0.002828147,"about_ca_topic_candidate":true,"about_ca_topic_consensus":true,"about_ca_topic_score_codex":0.6080253,"about_ca_topic_score_gemma":0.4506463,"domain_scores_codex":[0.999419,0.00008446939,0.0000593511,0.0001118863,0.0001845822,0.0001407679],"domain_scores_gemma":[0.9994341,0.0002264337,0.00008764423,0.00002348312,0.0001400924,0.00008819821],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"case_report","study_design_gemma":"observational","study_design_scores_codex":[0.004078979,0.0002795149,0.2367001,0.0005905626,0.0008758359,0.5039286,0.01067962,0.004460814,0.1333105,0.01975722,0.01303456,0.07230382],"study_design_scores_gemma":[0.0003425524,0.0003549631,0.5962641,0.0002713829,0.0008541266,0.3251705,0.004555312,0.007781948,0.02351188,0.003104323,0.03748561,0.0003033269],"study_design_candidate":"observational","study_design_consensus":null,"genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9845323,0.002237221,0.001055325,0.00140435,0.0001080887,0.00002994931,0.001204297,0.00009267763,0.009335864],"genre_scores_gemma":[0.99382,0.0004547469,0.0007971441,0.0001389525,0.00003961286,0.00001081085,0.000180956,0.00003258866,0.004525221],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.3919747,"threshold_uncertainty_score":0.7885662,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.005490824152865401,"score_gpt":0.1925617830933145,"score_spread":0.1870709589404491,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}