{"id":"W7105137606","doi":"10.71781/31545","title":"Caractérisation du role physiopathologique de LRPPRC chez la souris en réponse a une déficience hépato-spécifique et lors de l'expression de la mutation A354V de manière ubiquitaire.","year":2024,"lang":"fr","type":"dissertation","venue":"Papyrus : Institutional Repository (Université de Montréal)","topic":"Mitochondrial Function and Pathology","field":"Biochemistry, Genetics and Molecular Biology","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"","funders":"","keywords":"Animal model; Mitochondrial DNA; Mutation; Pentatricopeptide repeat","routes":{"ca_aff":false,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":true},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0002593795,0.0002850642,0.0002501572,0.0004391261,0.0002475461,0.0004107665,0.000229796,0.0008324145,0.002852241],"category_scores_gemma":[0.0002114254,0.0002016928,0.0004390499,0.000246184,0.0005839582,0.0003137002,0.0001861327,0.0006132573,0.0006460075],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0003346756,"about_ca_system_score_gemma":0.0001267557,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.002466989,"about_ca_topic_score_gemma":0.00103276,"domain_scores_codex":[0.9997731,0.0000323387,0.00001524794,0.00006892268,0.00004531156,0.00006516923],"domain_scores_gemma":[0.9998202,0.00003913126,0.00004987697,0.00002211024,0.00003235614,0.00003648228],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"bench_or_experimental","study_design_gemma":"bench_or_experimental","study_design_scores_codex":[0.0003824625,0.00005027403,0.004510771,0.00004726386,0.00001738984,0.001109587,0.0001434313,0.0000540312,0.9922443,0.0001173372,0.0001049499,0.001218174],"study_design_scores_gemma":[0.0000653833,0.00194131,0.2864544,0.00003687212,0.0001965916,0.01117661,0.001517129,0.001852634,0.6894851,0.0005043892,0.006723391,0.0000461446],"study_design_candidate":"bench_or_experimental","study_design_consensus":"bench_or_experimental","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.996646,0.001002721,0.0008476358,0.0001672737,0.00002559232,0.00001312369,0.0003729651,0.00004694381,0.0008778194],"genre_scores_gemma":[0.9964377,0.0004665376,0.0003237016,0.00007149301,0.000008060678,0.00001604885,0.0003936554,0.00001144229,0.002271349],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.002852241,"threshold_uncertainty_score":0.00954169,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.002913172548985057,"score_gpt":0.1949011324589074,"score_spread":0.1919879599099223,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}