{"id":"W7108682180","doi":"10.1182/blood-2025-3084","title":"Real-world treatment characteristics and outcomes in patients with von Willebrand disease treated prophylactically with plasma-derived or recombinant von Willebrand factor in europe: A multi-center, retrospective study","year":2025,"lang":"en","type":"article","venue":"Blood","topic":"Platelet Disorders and Treatments","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"Hotel Dieu Hospital; Group for Research in Decision Analysis","funders":"","keywords":"Von Willebrand disease; Retrospective cohort study; Von Willebrand factor; Medical record; Disease; Coagulopathy","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":false,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.0009729128,0.0002347035,0.0005463176,0.001872677,0.0003477257,0.0008479119,0.0003296819,0.0005492171,0.0009666681],"category_scores_gemma":[0.002247074,0.0002130124,0.0006189788,0.002536719,0.0003910931,0.0006631735,0.0003768483,0.0003112606,0.0001516856],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0005355896,"about_ca_system_score_gemma":0.0004100251,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.001818565,"about_ca_topic_score_gemma":0.001292214,"domain_scores_codex":[0.9987627,0.0003194026,0.0002733332,0.0003447386,0.0001744657,0.000125368],"domain_scores_gemma":[0.99685,0.0005093685,0.00193391,0.0001535297,0.0002325062,0.0003206322],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.0000902786,0.00002380082,0.9990045,0.00001367247,0.00006220761,0.00008754743,0.00002575456,0.00003551009,0.00004987703,0.00001248699,0.00005639505,0.0005379157],"study_design_scores_gemma":[0.0000237552,0.0002044883,0.9978194,0.00002093558,0.00007680247,0.0009272676,0.0002157811,0.0002144554,0.00007960613,0.00001602651,0.0003925319,0.000008846307],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9977477,0.0009343283,0.0001178838,0.00003155076,0.000005988968,0.00002188899,0.0007826982,0.000003198588,0.0003546596],"genre_scores_gemma":[0.9989115,0.0002079521,0.00009162811,0.00003060076,0.00001195314,0.00001872308,0.0006915569,0.000001533949,0.00003465438],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.001872677,"threshold_uncertainty_score":0.005145311,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.01048678238269008,"score_gpt":0.2530740349533118,"score_spread":0.2425872525706217,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}