{"id":"W7128093247","doi":"10.1093/eurheartj/ehaf784.2275","title":"Interim results from MyCLIMB, a natural history study of pediatric MYBPC3-associated hypertrophic cardiomyopathy","year":2025,"lang":"en","type":"article","venue":"European Heart Journal","topic":"Cardiomyopathy and Myosin Studies","field":"Medicine","cited_by":0,"is_retracted":false,"has_abstract":true,"ca_institutions":"University of Alberta Hospital","funders":"","keywords":"Natural history; Hypertrophic cardiomyopathy; Asymptomatic; Natural history study; Cardiomyopathy; Family history; Disease; Retrospective cohort study; Heart disease","routes":{"ca_aff":true,"ca_fund":false,"ca_venue":false,"about_ca":true,"invisible_to_affiliation_only":false},"retraction":null,"screen":null,"direct_labels":[],"prediction":{"model_version":"metacan-v3-hybrid-931329e0061c","candidate_categories":[],"consensus_categories":[],"category_scores_codex":[0.002523266,0.0003403956,0.0003562654,0.0009974682,0.0006248722,0.0007424148,0.0004051171,0.0002875159,0.002516001],"category_scores_gemma":[0.003041575,0.0002511514,0.0003286313,0.0009048505,0.0003640661,0.0004788648,0.001068092,0.0002454593,0.0006598391],"about_ca_system_candidate":false,"about_ca_system_consensus":false,"about_ca_system_score_codex":0.0005161896,"about_ca_system_score_gemma":0.0005224892,"about_ca_topic_candidate":false,"about_ca_topic_consensus":false,"about_ca_topic_score_codex":0.0020816,"about_ca_topic_score_gemma":0.003178176,"domain_scores_codex":[0.9989618,0.0003952686,0.00008999358,0.0002400099,0.000166466,0.0001463491],"domain_scores_gemma":[0.9961795,0.0008456375,0.0008653639,0.0006064922,0.000575328,0.0009277529],"domain_codex":null,"domain_gemma":null,"domain_candidate":null,"domain_consensus":null,"study_design_codex":"observational","study_design_gemma":"observational","study_design_scores_codex":[0.000691075,0.0000729389,0.9937019,0.00002107368,0.00005021659,0.0003588577,0.0001410518,0.00007683881,0.0008711842,0.00003613904,0.0008022446,0.003176533],"study_design_scores_gemma":[0.00006291466,0.0006394667,0.9957942,0.00001068789,0.00005858003,0.001069278,0.0001667278,0.0001477941,0.0004434499,0.00004120299,0.001556477,0.000009196893],"study_design_candidate":"observational","study_design_consensus":"observational","genre_codex":"empirical","genre_gemma":"empirical","genre_scores_codex":[0.9867115,0.0002431115,0.0006126802,0.00008225802,0.000008377748,0.00009411467,0.01071414,0.00003497026,0.001498774],"genre_scores_gemma":[0.9811928,0.0001387846,0.001100595,0.00009494612,0.00003917581,0.0002429677,0.01633037,0.00002635857,0.0008339954],"genre_candidate":"empirical","genre_consensus":"empirical","teacher_disagreement_score":0.002523266,"threshold_uncertainty_score":0.01334441,"prediction_status":"machine_predicted_unvalidated"},"machine_scores":{"provisional":true,"baseline":true,"maturity_gate_passed":false,"score_opus":0.04578926267476434,"score_gpt":0.2912866122489543,"score_spread":0.2454973495741899,"validation_status":"score_only:v0-immature-baseline","note":"Baseline scores from an immature model (maturity gate not passed). Scores rank; they never assert a category."}}