Orbital Anthropometrics Correct to Age-Matched Values after Strip Craniectomy in Metopic Craniosynostosis
Notice bibliographique
Résumé
BACKGROUND: Children with metopic craniosynostosis have distinct orbital dysmorphologies that include perceived hypotelorism and a symmetric, elliptical orbital aperture canted toward the synostosed suture. The extent to which hypotelorism is a true skeletal difference or, rather, perceived hypotelorism in the setting of trigonocephaly has been previously debated (1). Additionally, maneuvers to address the intercanthal distance during traditional fronto-orbital advancement procedures yield inconsistent results on orbital anthropometrics. The purpose of this study is to expand on our previous work by detailing pre- and post-operative orbital anthropometrics among a cohort of metopic synostosis patients undergoing endoscopic strip craniectomy (ESC) compared to age-matched controls. We aim to (1) detail the presence/absence of true skeletal hypotelorism in young infants with metopic synostosis and (2) define the role of ESC in restoring orbital anthropometric parameters to normal values. METHODS: A retrospective, cohort study was performed at a single center over a three-year (2020 – 2023) period. Using Slicer software, a three-dimensional craniometric analysis was performed on preoperative and one-year postoperative CT images of children with metopic craniosynostosis and age-matched peers. Twelve craniometric parameters were obtained. Age-matched children with normocephalic head shapes who underwent CT scan for other reasons than to rule-out craniosynostosis were utilized for comparison. RESULTS: Nine children were included as subjects in the study and fourteen children were included as controls. The mean age of subjects at pre-operative CT scan was 69.3 days and 72.3 days for controls. The mean age of subjects at post-operative CT scan was 14.8 months and 14.3 months for controls, for a mean follow-up of 11.4 months after ESC. 64 orbits were analyzed. Pre-operative subject Dacryon to Dacryon (Da-Da) measurements showed a significant difference from controls (12.2 ± 0.54 millimeters v. 15.4 ± 0.53 millimeters; p=0.0007), while post-surgery, there was no significant difference (16.11 ± 0.67 millimeters v. 15.10 ± 0.50 mm; p=0.2392). Similarly, Zygomaticofrontal suture to Zygomaticofrontal suture (ZF-ZF) measurements revealed a significant pre-operative difference (61.3 ±1.25 millimeters v. 67.2 ± 2.38 millimeters; p=0.0238) with post-operative normalization (76.0 ± 1.22 millimeters v. 76.0 ± 1.19 millimeters; p=0.9767). The supraorbital notch to anterior nasal spine to supraorbital notch (SON-ANS-SON) angle also indicated significant pre-operative differences (39.9 ± 0.96 degrees v. 60.1 ± 3.06 degrees; p=0.0001), with post-operative measurements showing no significant difference from controls (49.6 ± 1.39 degrees v. 55.3 ± 2.00 degrees; p=0.0674). CONCLUSIONS: Previous work demonstrated improvement in interdacryon distance before and after endoscopic strip craniectomy. The present effort shows that orbital hypotelorism in young infants with metopic synostosis is a true skeletal difference from age-matched controls that corrects after endoscopic strip craniectomy.
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Comment cette classification a été obtenuedéplier
Prédiction machine sur la base complète
Imitation des enseignantsNi prévalence calibrée, ni vérité terrain. Validation humaine à venir. Le volet Gemma est une étiquette directe du modèle pour chaque travail de la base, lue sur la notice réduite au titre. Le volet Codex est un classifieur appris des 10 348 étiquettes directes de Codex et calibré sur les taux pondérés de l'échantillon; les champs sans appui suffisant ne portent aucun appel Codex. Le mode candidate est l'union des deux volets; le consensus est leur intersection. Ces sorties portent le statut machine_predicted_unvalidated et ne sont pas des étiquettes humaines.
Scores du classifieur distillé par catégorie (deux têtes)
| Catégorie | Codex | Gemma |
|---|---|---|
| Métarecherche | 0,000 | 0,001 |
| Méta-épidémiologie (sens strict) | 0,000 | 0,000 |
| Méta-épidémiologie (sens large) | 0,000 | 0,000 |
| Bibliométrie | 0,001 | 0,001 |
| Études des sciences et des technologies | 0,000 | 0,000 |
| Communication savante | 0,000 | 0,000 |
| Science ouverte | 0,000 | 0,000 |
| Intégrité de la recherche | 0,000 | 0,000 |
| Charge utile insuffisante (le modèle a refusé de juger) | 0,001 | 0,000 |
Scores machine (provisoires)
Les deux têtes enseignantes du modèle étudiant, lues sur ce travail. Un score ordonne la base pour la relecture; il n'affirme jamais une catégorie, et le statut de validation accompagne chaque rangée tel quel.
Scores de référence d'un modèle non mature (critères de maturité non atteints, 7 itérations). Un score ordonne; il n'affirme jamais une catégorie.
score_only:v0-immature-baseline · tel quel depuis la passe de notation : score_only signifie que le nombre peut ordonner les travaux, et qu'aucune étiquette de catégorie n'en découleClassification
machine, non validéePrédiction automatique; un appel candidat d’une seule source (Gemma direct ou Codex distillé), pas un consensus.
Le détail, modèle par modèle et score par score, se trouve en fin de page sous « Comment cette classification a été obtenue ».