Perioperative Care of a Pediatric Patient With PHACES Syndrome
Bibliographic record
Abstract
PHACE syndrome is a neurocutaneous syndrome that was originally described by Dr. Ilonia Frieden in 1996. The term PHACE is an acronym for the main components of the syndrome including: P osterior fossa malformations of the central nervous system (CNS); H emangioma typically involving the skin of the head or neck; A rterial lesions usually involving the cerebral vasculature; C ardiac abnormalities, most commonly aortic coarctation; and Eye abnormalities. When accompanied by ventral developmental defects, it is termed PHACES syndrome, with the “S” representing sternal cleft or supraumbilical raphe. Patients may present for a variety of surgical procedures including the airway, CNS or the heart. Airway compromise secondary to hemangiomas and the potential for alterations in cerebral blood flow due to abnormalities of the cerebral arterial vasculature present major challenges for the anesthetic management of these patients. The perioperative implications of PHACES syndrome are discussed and previous reports of anesthetic care are reviewed. J Med Cases • 2013;4(12):811-815 doi: http://dx.doi.org/10.4021/jmc1374w
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How this classification was reachedexpand
Full frame machine prediction
Teacher imitationNot calibrated prevalence, not ground truth. Human validation pending. The Gemma side is a direct model label for every work in the frame, read from the title-only record. The Codex side is a classifier learned from the 10,348 direct Codex labels and calibrated to design-weighted sample rates; fields without enough sample support carry no Codex call. Candidate is the union of the two sides; consensus is their intersection. These outputs are machine_predicted_unvalidated and are not human labels.
Distilled classifier scores by category (both heads)
| Category | Codex | Gemma |
|---|---|---|
| Metaresearch | 0.000 | 0.002 |
| Meta-epidemiology (narrow) | 0.001 | 0.000 |
| Meta-epidemiology (broad) | 0.001 | 0.000 |
| Bibliometrics | 0.001 | 0.001 |
| Science and technology studies | 0.001 | 0.001 |
| Scholarly communication | 0.001 | 0.001 |
| Open science | 0.001 | 0.001 |
| Research integrity | 0.002 | 0.003 |
| Insufficient payload (model declined to judge) | 0.001 | 0.000 |
Machine scores (provisional)
The two teacher heads of the student model, read on this work. A score orders the frame for review; it never asserts a category, and the validation status ships verbatim with every row.
Baseline scores from an immature model (maturity gate not passed, 7 training rounds). Scores rank; they never assert a category.
score_only:v0-immature-baseline · verbatim from the scoring run: score_only means the number may rank works, and no category label ships from itClassification
machine, unvalidatedMachine predicted; a candidate call from one source (direct Gemma or distilled Codex), not a consensus.
How this classification was reached, model by model and score by score, is at the end of the page under "How this classification was reached".