MétaCan
Menu
Back to cohort
Record W2105793348 · doi:10.1017/s0317167100009823

Marchiafava-Bignami Disease (MBD) in a Non-Alcoholic Patient: A Case Report

2010· article· en· W2105793348 on OpenAlexvenueno aff
Santosh B. Murthy, Ali Jawaid, John Bock, Salah U. Qureshi, Paul E. Schulz

Bibliographic record

VenueCanadian Journal of Neurological Sciences / Journal Canadien des Sciences Neurologiques · 2010
Typearticle
Languageen
FieldMedicine
TopicInfectious Encephalopathies and Encephalitis
Canadian institutionsnot available
Fundersnot available
KeywordsAction (physics)MedicinePsychology

Abstract

fetched live from OpenAlex

Marchiafava-Bignami disease (MBD) is a rare disease characterized by primary focal demyelination of the corpus callosum, although lesions involving the cerebellar peduncles and the cerebral hemispheres have also been reported. 1archiafava and Bignami, in 1903, first described the disease in three Italian patents with a history of red wine consumption. 2The patients typically present with neuropsychiatric complaints, dysarthria, tetraparesis, astasia-abasia, impaired consciousness and symptoms of inter hemispheric disconnection.Owing to a lack of specific clinical features, the modern diagnosis is almost always based entirely on the magnetic resonance image (MRI) findings. 3archiafava-Bignami disease has traditionally been described as a consequence of chronic alcohol abuse.However, the occurrence of the disease in non-alcoholics suggests that the precise etiology remains to be established. [4][5]5] Here, we describe an unusual presentation of MBD in a non-alcoholic. CASE REPORTA 45-year-old, left-handed, Caucasian, non-alcoholic industrial worker presented with a history of lapses in memory for over a year.His family also noticed changes in his behavior, although he remained oblivious to it.He had become much quieter and socially withdrawn.He had no weakness, numbness or tingling.There was no history of urinary incontinence or gait disturbance.He had an occupational exposure to acetone and methyl ethyl ketone over a period of 14 years.On neurological examination, the deep tendon reflexes were diminished bilaterally.Frontal release signs (glabellar and snout) were positive.The rest of the general neurologic examination was normal.A neuropsychiatric evaluation revealed marked impairment in immediate recall and episodic memory, language and attention.There were mild deficits on visuospatial and semantic testing.The basic metabolic panel and vasculitic workup were within normal limits.The MRI brain showed focal demyelination involving the genu and splenium of the corpus callosum (Figures 1,2).There was diffusion restriction in the corpus callosum and a corresponding subtle change on the apparent diffusion coefficient map.A lumbar puncture showed a normal glucose, proteins and cell count.The IgG synthesis and oligoclonal bands were within the normal range.A paraneo-plastic panel was unrevealing.The constellation of clinical symptoms, the radiological findings, and the lack of an alternate diagnosis suggested a diagnosis of probable MBD.

Fetched live from OpenAlex and de-inverted. Abstracts are not stored in this database: the inverted indexes are 8.6 GB of the frame’s 9.3 GB of text, and the host has 13 GB free.

How this classification was reachedexpand

Full frame machine prediction

Teacher imitation

Not calibrated prevalence, not ground truth. Human validation pending. The Gemma side is a direct model label for every work in the frame, read from the title-only record. The Codex side is a classifier learned from the 10,348 direct Codex labels and calibrated to design-weighted sample rates; fields without enough sample support carry no Codex call. Candidate is the union of the two sides; consensus is their intersection. These outputs are machine_predicted_unvalidated and are not human labels.

metaresearch head score (Codex)0.000
metaresearch head score (Gemma)0.003
Version: metacan-v3-hybrid-931329e0061cValidation status: machine_predicted_unvalidated
Candidate categoriesnone
Consensus categoriesnone
DomainCandidate signal: none · Consensus signal: none
Study designCandidate signal: Case report · Consensus signal: Case report
GenreCandidate signal: Empirical · Consensus signal: Empirical
Teacher disagreement score0.006
Threshold uncertainty score0.013

Distilled classifier scores by category (both heads)

CategoryCodexGemma
Metaresearch0.0000.003
Meta-epidemiology (narrow)0.0020.001
Meta-epidemiology (broad)0.0020.001
Bibliometrics0.0030.002
Science and technology studies0.0040.002
Scholarly communication0.0020.003
Open science0.0020.002
Research integrity0.0060.003
Insufficient payload (model declined to judge)0.0030.001

Machine scores (provisional)

The two teacher heads of the student model, read on this work. A score orders the frame for review; it never asserts a category, and the validation status ships verbatim with every row.

Baseline scores from an immature model (maturity gate not passed, 7 training rounds). Scores rank; they never assert a category.

Opus teacher head0.018
GPT teacher head0.267
Teacher spread0.249 · how far apart the two teachers sit on this one work
Validation statusscore_only:v0-immature-baseline · verbatim from the scoring run: score_only means the number may rank works, and no category label ships from it

Classification

machine, unvalidated

Machine predicted; a candidate call from one source (direct Gemma or distilled Codex), not a consensus.

The models applied no category: nothing in the taxonomy fit this work.
Study designCase report
Domainnot available
GenreEmpirical

How this classification was reached, model by model and score by score, is at the end of the page under "How this classification was reached".

Quick stats

Citations11
Published2010
Admission routes1
Has abstractyes

Explore more

Same venueCanadian Journal of Neurological Sciences / Journal Canadien des Sciences NeurologiquesSame topicInfectious Encephalopathies and EncephalitisFrench-language works237,207