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Record W2885075424 · doi:10.1016/j.jdcr.2018.06.017

Infantile-onset palmo-plantar basal cell carcinomas and pits in Gorlin syndrome

2018· article· en· W2885075424 on OpenAlex

Why this work is in the frame

A frame that forgets how it found something cannot be audited. These are the routes that admitted this work.

affAt least one author lists a Canadian institution in the pinned OpenAlex snapshot.

Bibliographic record

VenueJAAD Case Reports · 2018
Typearticle
Languageen
FieldBiochemistry, Genetics and Molecular Biology
TopicHedgehog Signaling Pathway Studies
Canadian institutionsUniversité Laval
Fundersnot available
KeywordsNevoid basal-cell carcinoma syndromePTCH1HypertelorismPatchedBasal Cell Nevus SyndromeMacrocephalyBasal cell carcinomaMedicineFrontal BossingSmoothenedPathologyCancer researchHedgehogBiologyAnatomyBasal cellGeneGenetics

Abstract

fetched live from OpenAlex

Gorlin syndrome (also known as nevoid basal cell carcinoma syndrome [NBCCS]) is caused by an autosomal-dominant mutation in patched tumor suppressor genes 1 and 2 (PTCH1, PTCH2), or suppressor of fused homolog (SUFU) genes, involved in the hedgehog pathway. It carries a variable expressivity1 and manifests with a typical facies (macrocephaly, frontal bossing, coarse features, hypertelorism), palmo-plantar pits, multiple basal cell carcinomas (especially of the face, back, and chest1), and a propensity for other tumors (medulloblastomas, cardiac, and ovarian fibromas), among other features.

Fetched live from OpenAlex and de-inverted. Abstracts are not stored in this database: the inverted indexes are 8.6 GB of the frame’s 9.3 GB of text, and the host has 13 GB free.

Full frame distilled prediction

Teacher imitation

Not calibrated prevalence, not ground truth. Human validation pending. Learned from the 10,348 direct Codex labels and 10,348 direct Gemma labels. Candidate is the union of thresholded teacher heads; consensus is their intersection. These outputs are machine_predicted_unvalidated and are not human labels or direct frontier model labels.

metaresearch head score (Codex)0.000
metaresearch head score (Gemma)0.000
Version: codex-gemma-dda1882f352aValidation status: machine_predicted_unvalidated
Candidate categoriesnone
Consensus categoriesnone
DomainCandidate signal: none · Consensus signal: none
Study designCandidate signal: Bench or experimental · Consensus signal: none
GenreCandidate signal: Empirical · Consensus signal: Empirical
Teacher disagreement score0.420
Threshold uncertainty score0.800

Codex and Gemma teacher scores by category

CategoryCodexGemma
Metaresearch0.0000.000
Meta-epidemiology (narrow)0.0000.000
Meta-epidemiology (broad)0.0000.000
Bibliometrics0.0000.000
Science and technology studies0.0000.000
Scholarly communication0.0000.000
Open science0.0000.000
Research integrity0.0000.000
Insufficient payload (model declined to judge)0.0000.000

Machine scores (provisional)

The two teacher heads of the student model, read on this work. A score orders the frame for review; it never asserts a category, and the validation status ships verbatim with every row.

Baseline scores from an immature model (maturity gate not passed, 7 training rounds). Scores rank; they never assert a category.

Opus teacher head0.009
GPT teacher head0.237
Teacher spread0.228 · how far apart the two teachers sit on this one work
Validation statusscore_only:v0-immature-baseline · verbatim from the scoring run: score_only means the number may rank works, and no category label ships from it