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Record W2890220586 · doi:10.1136/jnnp-2018-ehdn.175

G01 Huntington disease predictive testing protocol: a 5 year review of practice

2018· article· en· W2890220586 on OpenAlexaff
Claire Goldsmith, Kym M. Boycott

Bibliographic record

Venuenot available
Typearticle
Languageen
FieldNeuroscience
TopicGenetic Neurodegenerative Diseases
Canadian institutionsChildren's Hospital of Eastern Ontario
Fundersnot available
KeywordsHelpfulnessProtocol (science)Predictive testingMedicinePsychosocialTest (biology)Genetic testingReferralPhysical therapyClinical psychologyPsychologyPsychiatryInternal medicineFamily medicinePathologyAlternative medicineSocial psychology

Abstract

fetched live from OpenAlex

Background The protocol for HD predictive testing at our Centre includes a psychosocial assessment as step 2 of a 3-step process. In future, this resource may not be available. Aims To review our experience with our HD predictive testing protocol. Methods We performed a 5-year review of patients referred for pre-symptomatic testing for HD and solicited feedback from 10 recent patients. Results/outcome A total of 104 individuals at 50% risk requested predictive testing for HD. The majority (87; 84%) completed the protocol and received results. Almost all agreed to meet a neuropsychiatrist and none were flagged as poor candidates for predictive testing. Of the 17 that did not complete the protocol, 13 (76.5%) discontinued after the first session with the genetic counsellor, 2 never returned for results, 1 stopped after blood test, and 1 saw neuropsychiatrist but never had blood drawn. Conversations with the 10 most recent patients revealed that most felt the process worked well. Wait-time for results was the only complaint. Opinions differed regarding the helpfulness of neuropsychiatric consultation and few patients opted to access neuropsychiatry after the protocol was complete. Conclusions Assessing readiness is essential to HD predictive testing, as is psychological support after testing. Feedback from our patients was mixed with regard to usefulness of meeting with neuropsychiatrist. The significant number of patients (12.5%) who did not continue with the protocol after first session with the genetic counsellor vs the small number (3%) who did so after the neuropsychiatric evaluation, suggests the majority of patients are making decisions very early on in the protocol.

Fetched live from OpenAlex and de-inverted. Abstracts are not stored in this database: the inverted indexes are 8.6 GB of the frame’s 9.3 GB of text, and the host has 13 GB free.

How this classification was reachedexpand

Full frame machine prediction

Teacher imitation

Not calibrated prevalence, not ground truth. Human validation pending. The Gemma side is a direct model label for every work in the frame, read from the title-only record. The Codex side is a classifier learned from the 10,348 direct Codex labels and calibrated to design-weighted sample rates; fields without enough sample support carry no Codex call. Candidate is the union of the two sides; consensus is their intersection. These outputs are machine_predicted_unvalidated and are not human labels.

metaresearch head score (Codex)0.172
metaresearch head score (Gemma)0.259
Version: metacan-v3-hybrid-931329e0061cValidation status: machine_predicted_unvalidated
Candidate categoriesnone
Consensus categoriesnone
DomainCandidate signal: none · Consensus signal: none
Study designCandidate signal: Observational · Consensus signal: none
GenreCandidate signal: Review · Consensus signal: none
Teacher disagreement score0.172
Threshold uncertainty score0.911

Distilled classifier scores by category (both heads)

CategoryCodexGemma
Metaresearch0.1720.259
Meta-epidemiology (narrow)0.0010.002
Meta-epidemiology (broad)0.0020.003
Bibliometrics0.0110.008
Science and technology studies0.0030.003
Scholarly communication0.0070.008
Open science0.0070.008
Research integrity0.0080.006
Insufficient payload (model declined to judge)0.0130.013

Machine scores (provisional)

The two teacher heads of the student model, read on this work. A score orders the frame for review; it never asserts a category, and the validation status ships verbatim with every row.

Baseline scores from an immature model (maturity gate not passed, 7 training rounds). Scores rank; they never assert a category.

Opus teacher head0.053
GPT teacher head0.355
Teacher spread0.301 · how far apart the two teachers sit on this one work
Validation statusscore_only:v0-immature-baseline · verbatim from the scoring run: score_only means the number may rank works, and no category label ships from it

Classification

machine, unvalidated

Machine predicted; a candidate call from one source (direct Gemma or distilled Codex), not a consensus.

The models applied no category: nothing in the taxonomy fit this work.
Study designObservational
Domainnot available
GenreReview

How this classification was reached, model by model and score by score, is at the end of the page under "How this classification was reached".

Quick stats

Citations0
Published2018
Admission routes1
Has abstractyes

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