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Record W2971831830 · doi:10.1161/hyp.74.suppl_1.039

Abstract 039: The <i>PDE3A</i> Gene Regulates Blood Pressure

2019· article· en· W2971831830 on OpenAlexaff
Friedrich C. Luft, Maria Ercu, Carolin Schächterle, Lajos Markó, Philipp G. Maass, Kerstin Zühlke, Alexa Kidd, Nerine Gregersen, Norbert Hübner, Russell Hodge, Rosana Molé Illas, Stephan Walter, Robert Preißner, Arnd Heuser, Yoland‐Marie Anistan, D Tsvetkov, Mihail Todiraş, Elena Popova, Sofia K. Forslund, Dominik N. Müller, Maik Gollasch, Atakan Aydın, Sylvia Bähring, Michael Bäder, Enno Klußmann

Bibliographic record

VenueHypertension · 2019
Typearticle
Languageen
FieldMedicine
TopicHormonal Regulation and Hypertension
Canadian institutionsSickKids Foundation
Fundersnot available
KeywordsBlood pressureInternal medicineEndocrinologyMedicineBrachydactylyPhenotypeMutantAmino acidBiologyGeneGenetics

Abstract

fetched live from OpenAlex

Hypertension is the greatest driver of cardiovascular disease, the most common cause of death. Finding novel model mechanisms for blood-pressure (BP) regulation is an important goal. Autosomal-dominant hypertension with brachydactyly (HTNB) clinically resembles salt-resistant essential hypertension and causes death by stroke, commonly before age 50 years. We identified mutated phosphodiesterase 3A as responsible earlier; however, definitive mechanistic proof and animal models were lacking. We now describe new kindreds, one substituted within the earlier-described regulatory region (G449S), and another with a mutation causing an amino acid substitution within the PDE3A enzymatic pocket (R864C). Both exhibit the HTNB phenotype. Mutant PDE3A (T445N) overexpression in mouse vascular smooth muscle cells causes hypertension (mean telemetry BP 130/88 mm Hg vs littermate control 115/84 mm Hg, p&lt;0.01). A 9 base-pair, three amino acid (3AA) deletion within the regulatory segment (using CRISPR-Cas9 technology), recapitulates HTNB in the rat, including the skeletal (with micro CT) phenotype. Three-weeks of radiotelemetry in homozygous 3AA+/+ rats at age 6 months revealed mean systolic BP 151, diastolic BP 119 mm Hg; heterozygous 3AA+/- (like the patients) showed 148/105 mm Hg; PDE3A knockout (frame-shift mutation) rats exhibited the lowest pressures at 115/87 mm Hg (all p&lt;0.001) vs. BP of wild-type Sprague-Dawley rats at mean 126/90 mm Hg. R864C causes increased oligomerization. Furthermore, R864C, T445N, and 3AA all cause increased interactions at the scaffolding protein, 14-3-3 theta, compared to the wild-type (P&lt;0.05). With two separate rodent models, our data not only direct mechanistic hypertension research along non-renal pathways, but also identify new areas of possible therapeutic intervention. We suggest that PDE3A could represent a generalizable novel therapeutic target in all instances of elevated blood pressure.

Fetched live from OpenAlex and de-inverted. Abstracts are not stored in this database: the inverted indexes are 8.6 GB of the frame’s 9.3 GB of text, and the host has 13 GB free.

How this classification was reachedexpand

Full frame distilled prediction

Teacher imitation

Not calibrated prevalence, not ground truth. Human validation pending. Learned from the 10,348 direct Codex labels and 10,348 direct Gemma labels. Candidate is the union of thresholded teacher heads; consensus is their intersection. These outputs are machine_predicted_unvalidated and are not human labels or direct frontier model labels.

metaresearch head score (Codex)0.000
metaresearch head score (Gemma)0.000
Version: codex-gemma-dda1882f352aValidation status: machine_predicted_unvalidated
Candidate categoriesInsufficient payload (model declined to judge)
Consensus categoriesnone
DomainCandidate signal: none · Consensus signal: none
Study designCandidate signal: Bench or experimental · Consensus signal: none
GenreCandidate signal: Empirical · Consensus signal: Empirical
Teacher disagreement score0.883
Threshold uncertainty score1.000

Codex and Gemma teacher scores by category

CategoryCodexGemma
Metaresearch0.0000.000
Meta-epidemiology (narrow)0.0000.000
Meta-epidemiology (broad)0.0000.000
Bibliometrics0.0000.000
Science and technology studies0.0000.000
Scholarly communication0.0000.000
Open science0.0000.000
Research integrity0.0000.000
Insufficient payload (model declined to judge)0.0000.001

Machine scores (provisional)

The two teacher heads of the student model, read on this work. A score orders the frame for review; it never asserts a category, and the validation status ships verbatim with every row.

Baseline scores from an immature model (maturity gate not passed, 7 training rounds). Scores rank; they never assert a category.

Opus teacher head0.018
GPT teacher head0.224
Teacher spread0.206 · how far apart the two teachers sit on this one work
Validation statusscore_only:v0-immature-baseline · verbatim from the scoring run: score_only means the number may rank works, and no category label ships from it

Classification

machine, unvalidated

Machine predicted; a candidate call from one teacher head, not a consensus.

Study designBench or experimental
Domainnot available
GenreEmpirical

How this classification was reached, model by model and score by score, is at the end of the page under "How this classification was reached".

Quick stats

Citations1
Published2019
Admission routes1
Has abstractyes

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