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Record W4206457317 · doi:10.1038/s41467-021-27132-8

A de novo paradigm for male infertility

2022· article· en· W4206457317 on OpenAlex
Manon S. Oud, RM Smits, H E Smith, Francesco Mastrorosa, Giles Holt, Brendan J. Houston, Petra F. de Vries, B. Alobaidi, Lois E. Batty, Hoda Ismail, Joel Greenwood, Harsh Sheth, Aneta Mikulášová, Galuh Astuti, Christian Gilissen, Kevin McEleny, H Turner, Jonathan Coxhead, Simon Cockell, D.D.M. Braat, Kathrin Fleischer, K. W. M. D’Hauwers, Ewout Schaafsma, Donald F. Conrad, Liina Nagirnaja, Kenneth I. Aston, Douglas T. Carrell, James M. Hotaling, Timothy Jenkins, Rob McLachlan, Moira K. O’Bryan, Peter N. Schlegel, Michael L. Eisenberg, Jay Sandlow, Emily S. Jungheim, Kenan Omurtag, Alexandra M. Lopes, Susana Seixas, Filipa Carvalho, Susana Fernandes, Alberto Barros, João Gonçalves, Graça Pinto, Sónia Vladimira Correia, Maris Laan, Margus Punab, Ewa Rajpert‐De Meyts, Niels Jørgensen, Kristian Almstrup, Csilla Krausz, Keith Jarvi, Corinna Friedrich, Sabine Kliesch, Antoni Riera‐Escamilla, Claudia Gonzaga‐Jauregui, Mauro Santibanez‐Koref, David J. Elliott, Lisenka E.L.M. Vissers, Frank Tüttelmann, Liliana Ramos, Miguel J. Xavier, Godfried W. van der Heijden, Joris A. Veltman

Why this work is in the frame

A frame that forgets how it found something cannot be audited. These are the routes that admitted this work.

affAt least one author lists a Canadian institution in the pinned OpenAlex snapshot.

Bibliographic record

VenueNature Communications · 2022
Typearticle
Languageen
FieldBiochemistry, Genetics and Molecular Biology
TopicGenetic and Clinical Aspects of Sex Determination and Chromosomal Abnormalities
Canadian institutionsUniversity of TorontoMount Sinai Hospital
FundersEunice Kennedy Shriver National Institute of Child Health and Human DevelopmentNational Institute of Mental HealthNational Health and Medical Research CouncilBiotechnology and Biological Sciences Research CouncilRadboud Universitair Medisch CentrumMonash UniversityWestfälische Wilhelms-Universität MünsterDeutsche ForschungsgemeinschaftDirectorate for Biological SciencesNational Institutes of HealthNewcastle UniversityNederlandse Organisatie voor Wetenschappelijk OnderzoekWellcome TrustMedical Research CouncilWellcome
KeywordsMissense mutationInfertilityGeneticsMale infertilityBiologyGeneExome sequencingPhenotypeLoss functionMutationAzoospermiaPregnancy

Abstract

fetched live from OpenAlex

Abstract De novo mutations are known to play a prominent role in sporadic disorders with reduced fitness. We hypothesize that de novo mutations play an important role in severe male infertility and explain a portion of the genetic causes of this understudied disorder. To test this hypothesis, we utilize trio-based exome sequencing in a cohort of 185 infertile males and their unaffected parents. Following a systematic analysis, 29 of 145 rare (MAF < 0.1%) protein-altering de novo mutations are classified as possibly causative of the male infertility phenotype. We observed a significant enrichment of loss-of-function de novo mutations in loss-of-function-intolerant genes ( p -value = 1.00 × 10 −5 ) in infertile men compared to controls. Additionally, we detected a significant increase in predicted pathogenic de novo missense mutations affecting missense-intolerant genes ( p -value = 5.01 × 10 −4 ) in contrast to predicted benign de novo mutations. One gene we identify, RBM5 , is an essential regulator of male germ cell pre-mRNA splicing and has been previously implicated in male infertility in mice. In a follow-up study, 6 rare pathogenic missense mutations affecting this gene are observed in a cohort of 2,506 infertile patients, whilst we find no such mutations in a cohort of 5,784 fertile men ( p -value = 0.03). Our results provide evidence for the role of de novo mutations in severe male infertility and point to new candidate genes affecting fertility.

Fetched live from OpenAlex and de-inverted. Abstracts are not stored in this database: the inverted indexes are 8.6 GB of the frame’s 9.3 GB of text, and the host has 13 GB free.

Full frame distilled prediction

Teacher imitation

Not calibrated prevalence, not ground truth. Human validation pending. Learned from the 10,348 direct Codex labels and 10,348 direct Gemma labels. Candidate is the union of thresholded teacher heads; consensus is their intersection. These outputs are machine_predicted_unvalidated and are not human labels or direct frontier model labels.

metaresearch head score (Codex)0.000
metaresearch head score (Gemma)0.000
Version: codex-gemma-dda1882f352aValidation status: machine_predicted_unvalidated
Candidate categoriesnone
Consensus categoriesnone
DomainCandidate signal: none · Consensus signal: none
Study designCandidate signal: Not applicable · Consensus signal: none
GenreCandidate signal: Empirical · Consensus signal: Empirical
Teacher disagreement score0.796
Threshold uncertainty score0.318

Codex and Gemma teacher scores by category

CategoryCodexGemma
Metaresearch0.0000.000
Meta-epidemiology (narrow)0.0000.000
Meta-epidemiology (broad)0.0000.000
Bibliometrics0.0000.000
Science and technology studies0.0000.000
Scholarly communication0.0000.000
Open science0.0010.000
Research integrity0.0000.000
Insufficient payload (model declined to judge)0.0000.000

Machine scores (provisional)

The two teacher heads of the student model, read on this work. A score orders the frame for review; it never asserts a category, and the validation status ships verbatim with every row.

Baseline scores from an immature model (maturity gate not passed, 7 training rounds). Scores rank; they never assert a category.

Opus teacher head0.021
GPT teacher head0.316
Teacher spread0.295 · how far apart the two teachers sit on this one work
Validation statusscore_only:v0-immature-baseline · verbatim from the scoring run: score_only means the number may rank works, and no category label ships from it