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Record W4224242276 · doi:10.1016/s2352-4642(22)00095-5

Worldwide trends in population-based survival for children, adolescents, and young adults diagnosed with leukaemia, by subtype, during 2000–14 (CONCORD-3): analysis of individual data from 258 cancer registries in 61 countries

2022· article· en· W4224242276 on OpenAlexafffundabout
Naomi Ssenyonga, Charles Stiller, Kayo Nakata, Jaime Shalkow‐Klincovstein, S M Redmond, Jean‐Luc Bulliard, Fabio Girardi, Christine Fowler, Rafael Marcos‐Gragera, Audrey Bonaventure, Nathalie Saint‐Jacques, Pamela Minicozzi, Prithwish De, Miguel Rodríguez‐Barranco, Siri Larønningen, V Di Carlo, Margit Mägi, М. Yu. Valkov, Karri Seppä, Dyfed Huws, Michel P. Coleman, Claudia Allemani, S. Bouzbid, M Hamdi-Chérif, Kaouel Meguenni, D. Regagba, Siné Bayo, T Cheick Bougadari, Shyam Manraj, Karima Bendahhou, A Ladipo, Olufemi J. Ogunbiyi, Nontuthuzelo Somdyala, M A Chaplin, Florencia Moreno, Gladis Calabrano, Silvia Espinola, B Carballo Quintero, Rosalba Fita, Walter Laspada, Susana Ibañez, Carlos Anselmo Lima, Allini Mafra da Costa, Paulo César De Souza, J. Chaves, C. Laporte, María Paula Curado, José Carlos de Oliveira, Claudia Veneziano, Donaldo Botelho Veneziano, Ana Beatriz Almeida, Maria do Rosário Dias de Oliveira Latorre, Gulnar Azevedo e Silva, Marise Souto Rebelo, M O Santos, J.C. Galaz, M Aparicio Aravena, J Sanhueza Monsalve, D.A. Herrmann, Solange Vargas, Víctor Herrera, Claudia Uribe, Luis Eduardo Bravo, Luz Stella García, Nelson Enrique Arias-Ortiz, D Morantes, Daniel Jurado, María Yépez Chamorro, Sandra Delgado, Melissa Ramirez, Yaíma Galán Álvarez, Priscila Torres, F Martínez-Reyes, J Castillo, Mariela Mendoza, Patricia Cueva, José Yépez, Bernard Bhakkan, Jacqueline Deloumeaux, Clarisse Joachim, Jonathan Macni, R Carrillo, Jaime Shalkow Klincovstein, Rebeca Rivera-Gómez, Patricia Pérez, Ebert Poquioma, Guillermo Tortolero‐Luna, Diego Zavala, R. Alonso, Enrique Barrios, Angela Eckstrand, C Nikiforuk, Ryan Woods, Glen Noonan, Donna Turner, Eshwar Kumar, Bin Zhang, Jeff Dowden, Gregory Doyle, Gordon Walsh, Aniq Anam, Carol McClure, K.A. Vriends, Christine Bertrand, Agnihotram V. Ramanakumar, Serena Kozie, H. Stuart-Panko, T Freeman, Justin George, Rosa M. Avila, David K. O’Brien, A Holt, Lyn Almon, Kevin C. Ward, Sandy Kwong, Cyllene R. Morris, Randi Rycroft, Lloyd Mueller, Cathryn Phillips, Heather M. Brown, B Cromartie, Julie J. Ruterbusch, Ann G. Schwartz, Gary M. Levin, Brad Wohler, Rana Bayakly, Scarlett Lin Gomez, Meg McKinley, Rosemary D. Cress, Joni Davis, Brenda Y. Hernandez, Christopher J. Johnson, Bożena M Morawski, Laura Ruppert, Suzanne Bentler, Mary E. Charlton, Bin Huang, T. C. Tucker, Dennis Deapen, Lihua Liu, Mei‐Chin Hsieh, Xiao‐Cheng Wu, Molly Schwenn, Kimberly J. Stern, Susan N. Gershman, Richard Knowlton, Georgetta Alverson, Tamara Weaver, Jay Desai, Deirdre Rogers, J Jackson-Thompson, D Lemons, Heather Zimmerman, Michelle M. Hood, J Roberts-Johnson, Whitney Hammond, Judith R Rees, Karen Pawlish, Antoinette M. Stroup, Charles R. Key, Charles L. Wiggins, Amy R. Kahn, Maria J. Schymura, Soundarya Radhakrishnan, Chandrika Rao, L K Giljahn, R M Slocumb, C Dabbs, Raffaella Espinoza, K G Aird, T Beran, J J Rubertone, S J Slack, Junhie Oh, T A Janes, Stephen M. Schwartz, S Chiodini, Deborah Hurley, Martin Whiteside, Saroj Rai, Melanie Williams, Kim Herget, Carol Sweeney, Alison Johnson, Mahesh Keitheri Cheteri, Patti Migliore Santiago, S. R. Blankenship, Shawn Farley, Robert R. Borchers, R Malicki, J.R. Espinoza, Joseph Grandpre, Brenda K. Edwards, A Mariotto, Hannah K Weir, Reda Wilson, Ning Wang, Lei Yang, Jian-Shun Chen, Yutong He, Guohui Song, Xiaoping Gu, Dan Mei, Heng-Ming Ge, Tonghao Wu, Yanyan Li, Deli Zhao, Feng Jin, Jianhua Zhang, Feng-Dong Zhu, Q Junhua, Yan Lei Yang, Chunxiao Jiang, Jian Wang, Qilong Li, Yi He, Xin Zhou, Jianmei Dong, Weiwei Li, F X Fu, Jianguo Chen, Jian Zhu, Yanhua Li, Yuqiang Lu, Min Fan, Suqin Huang, Guo‐Ping Guo, Hua Zhao-lai, Kuangrong Wei, Wanqing Chen, Wenqiang Wei, Hongmei Zeng, Anna Demetriou, W.K. Mang, K.C. Ngan, Amal Chandra Kataki, Manigreeva Krishnatreya, P A Jayalekshmi, Paul Sebastian, Preethi Sara George, Aleyamma Mathew, Ambakumar Nandakumar, Reza Malekzadeh, Gholamreza Roshandel, Lital Keinan-Boker, Barbara Silverman, Hidemi Ito, Yuriko N. Koyanagi, Masako Satô, F Tobori, Ichiro Nakata, Teramoto Norihiro, Masakazu Hattori, Yasuharu Kaizaki, Fumitaka Moki, Hiromi Sugiyama, Mai Utada, Keiichi YOSHIDA, K Kurosawa, Y Nemoto, Hiroto Narimatsu, Masahiko Sakaguchi, Seiki Kanemura, Michiko Naito, Rintaro Narisawa, Isao Miyashiro, Daisuke Mori, Mayuko Yoshitake, Izumi Oki, Norimasa Fukushima, Akiko Shibata, K Iwasa, Chie Ono, Tomohiro Matsuda, Omar Nimri, Kyu‐Won Jung, Young‐Joo Won, Eiman Alawadhi, A Elbasmi, Azizah Ab Manan, Farzaana Adam, Erdenekhuu Nansalmaa, Undarmaa Tudev, Chimedsuren Оchir, ABD EL RAHMAN KHATER, Mufid El Mistiri, Gek Hsiang Lim, Yik Ying Teo, Chun‐Ju Chiang, Wen‐Chung Lee, R Buasom, Suleeporn Sangrajrang, Krittika Suwanrungruang, Patravoot Vatanasapt, Karnchana Daoprasert, Donsuk Pongnikorn, Atit Leklob, S Sangkitipaiboon, Sarayut Lucien Geater, Hutcha Sriplung, İskender Kög, Oya Dirican, T Köse, T Gurbuz, F E Karaşahin, Duygu Özhan Turhan, U Aktaş, Y Halat, Sultan Eser, Cankut Yakut, Merve Altinisik, Y Cavusoglu, A Türkköylü, N Üçüncü, Monika Hackl, A. Zborovskaya, Olga Aleinikova, K. Henau, Liesbet Van Eycken, Trayan Atanasov, Z. Valerianova, Mario Šekerija, Ladislav Dušek, Miroslav Zvolský, Lina Steinrud Mørch, Hans H. Storm, Charlotte Wessel Skovlund, Kaire Innos, Nea Malila, Jérémie Jegu, Michel Velten, Édouard Cornet, Xavier Troussard, Anne‐Marie Bouvier, Anne‐Valérie Guizard, Véronique Bouvier, Guy Launoy, Sandrine Dabakuyo Yonli, Marie‐Laure Poillot, Marc Maynadié, Morgane Mounier, L Vaconnet, Anne‐Sophie Woronoff, M. Daoulas, Michel Robaszkiewicz, Jacqueline Clavel, Claire Poulalhon, Emmanuel Désandes, Brigitte Lacour, Isabelle Baldi, Camille Pouchieu, Brice Amadéo, Gaëlle Coureau, Alain Monnereau, Tania d’Almeida, Séverine Boyer, Karima Hammas, Brigitte Trétarre, Marc Colonna, Patricia Delafosse, Sandrine Plouvier, Anne Cowppli‐Bony, Florence Molinié, Simona Bara, O. Ganry, B. Lapôtre‐Ledoux, Laëtitia Daubisse‐Marliac, Nadine Bossard, Jacques Estève, Zoé Uhry, Roland Stabenow, Heide Wilsdorf-Köhler, Andrea Eberle, Sabine Luttmann, I Löhden, Alice Nennecke, Joachim Kieschke, Eunice Sirri, Christina Justenhoven, Sylke Zeissig, Bernd Holleczek, Nora Eisemann, Alexander Katalinic, Rachelle Asquez, Vijay Kumar, Eleni Petridou, Laufey Tryggvadóttír, Deirdre M. Murray, H Sundseth, Guido Mazzoleni, Fabio Vittadello, Enzo Coviello, Francesco Cuccaro, Rocco Galasso, Giuseppe Sampietro, Michele Magoni, A Ardizzone, Angelo D’Argenzio, Alessia Anna Di Prima, Antonella Ippolito, Anna Maria Lavecchia, Antonella Sutera Sardo, G Gola, Paola Ballotari, Erica Giacomazzi, Stefano Ferretti, Luigino Dal Maso, Diego Serraino, M V Celesia, Rosa Angela Filiberti, Fabio Pannozzo, Anna Melcarne, F Quarta, Anita Andreano, Antonio Russo, Giuliano Carrozzi, Claudia Cirilli, Luca Cavalieri d’Oro, M Rognoni, Mario Fusco, Maria Francesca Vitale, M. Usala, Rosanna Cusimano, Walter Mazzucco, Maria Michiara, Paolo Sgargi, Lorenza Boschetti, Giorgio Chiaranda, Pietro Seghini, Milena Maule, Franco Merletti, Eugenia Spata, ­Rosario ­Tumino, Pamela Mancuso, Massimo Vicentini, Tiziana Cassetti, Romano Sassatelli, Fabio Falcini, Stefania Giorgetti, Anna Luisa Caiazzo, Rossella Cavallo, Daniela Piras, Francesca Bella, A Madeddu, Anna Clara Fanetti, S. Maspero, Simona Carone, Antonia Mincuzzi, Giuseppa Candela, T. Scuderi, Maria Gentilini, Roberto Vito Rizzello, Stefano Rosso, Roberto Zanetti, Adele Caldarella, Teresa Intrieri, Fortunato Bianconi, Fabrizio Stracci, Paolo Contiero, Giovanna Tagliabue, Massimo Rugge, Manuel Zorzi, S Beggiato, Angelita Brustolin, Roberta De Angelis, Gemma Gatta, A Maurina, M Oniščuka, N. A. Lipunova, Ieva Vincerževskienė, Dominic Agius, Neville Calleja, Sabine Siesling, Otto Visser, Tom Børge Johannesen, Maciej Trojanowski, Tomasz Mierzwa, Jadwiga Rachtan, Kamila Kępska, Beata Kościańska, Joanna Wójcik-Tomaszewska, M Motnyk, Anna Gos, Magdalena Bielska‐Lasota, Joanna Didkowska, Urszula Wojciechowska, G. Forjaz de Lacerda, Raúl Rego, Branca Carrito, Ana Pais, María José Bento, Jéssica Rodrigues, Antonio Lourenço, A. Mayer-da-Silva, Luminita Blaga, Daniela Coza, L Gusenkova, O Lazarevich, О. Н. Прудникова, D M Vjushkov, A.G. Egorova, Andrey E. Orlov, L. V. Pikalova, Л. Д. Жуйкова, J Adamcik, C. Safaei Diba, Vesna Zadnik, Tina Žagar, Marta De-La-Cruz, Arantza López-de-Munain, Araceli Alemán, R J Chillarón, Ana Isabel Marcos Navarro, Montse Puigdemont, M. Perez, P. Franch Sureda, M. Ramos Montserrat, María Dolores Chirlaque López, A Sánchez Gil, Eva Ardanáz, Marcela Guevara, Adela Cañete-Nieto, Rafael Peris‐Bonet, Marià Carulla, Jaume Galcerán, Fernando Almela, Consol Sabater, Staffan Khan, David Pettersson, Paul W. Dickman, Katharina Staehelin, Benjamin Struchen, C. Herrmann, Seyed Mohsen Mousavi, Céline Egger Hayoz, Christine Bouchardy, Robin Schaffar, Philip Went, M. Maspoli-Conconi, Claudia E. Kuehni, Shelagh Redmond, Andrea Bordoni, Laura Ortelli, Arnaud Chioléro, Isabelle Konzelmann, Sabine Rohrmann, Miriam Wanner, John Broggio, Jem Rashbass, Deirdre Fitzpatrick, Anna Gavin, David Morrison, Catherine Thomson, Giles Greene, M Matz, Natalia Sanz, Richard Stephens, Elizabeth Chalker, Mirka Smith, Jessica Gugusheff, Hui You, Shu Qin Li, Sarah Dugdale, Julie Moore, Shoni Philpot, Rhonda Pfeiffer, Helen E. Thomas, Bruna S. Ragaini, Alison Venn, Sue Evans, Luc te Marvelde, Vedrana Savietto, Richard Trevithick, David C. Currow, Chris Lewis

Bibliographic record

VenueThe Lancet Child & Adolescent Health · 2022
Typearticle
Languageen
FieldMedicine
TopicAcute Lymphoblastic Leukemia research
Canadian institutionsDalhousie University
FundersNational Cancer InstituteBC Cancer AgencyLigue Contre le CancerACT GovernmentCenters for Disease Control and PreventionSwiss ReCHILDREN with CANCER UKCancer Care OntarioSwiss Cancer Research FoundationNew York City Department of Health and Mental HygienePennsylvania Department of HealthOhio Department of HealthInstitut National Du CancerCancer Research UKU.S. Department of Health and Human Services
KeywordsMedicineYoung adultCancerPopulationPediatricsDemographyCancer registrySurvival analysisGerontologyInternal medicineEnvironmental health

Abstract

fetched live from OpenAlex

BACKGROUND: Leukaemias comprise a heterogenous group of haematological malignancies. In CONCORD-3, we analysed data for children (aged 0-14 years) and adults (aged 15-99 years) diagnosed with a haematological malignancy during 2000-14 in 61 countries. Here, we aimed to examine worldwide trends in survival from leukaemia, by age and morphology, in young patients (aged 0-24 years). METHODS: We analysed data from 258 population-based cancer registries in 61 countries participating in CONCORD-3 that submitted data on patients diagnosed with leukaemia. We grouped patients by age as children (0-14 years), adolescents (15-19 years), and young adults (20-24 years). We categorised leukaemia subtypes according to the International Classification of Childhood Cancer (ICCC-3), updated with International Classification of Diseases for Oncology, third edition (ICD-O-3) codes. We estimated 5-year net survival by age and morphology, with 95% CIs, using the non-parametric Pohar-Perme estimator. To control for background mortality, we used life tables by country or region, single year of age, single calendar year and sex, and, where possible, by race or ethnicity. All-age survival estimates were standardised to the marginal distribution of young people with leukaemia included in the analysis. FINDINGS: 164 563 young people were included in this analysis: 121 328 (73·7%) children, 22 963 (14·0%) adolescents, and 20 272 (12·3%) young adults. In 2010-14, the most common subtypes were lymphoid leukaemia (28 205 [68·2%] patients) and acute myeloid leukaemia (7863 [19·0%] patients). Age-standardised 5-year net survival in children, adolescents, and young adults for all leukaemias combined during 2010-14 varied widely, ranging from 46% in Mexico to more than 85% in Canada, Cyprus, Belgium, Denmark, Finland, and Australia. Individuals with lymphoid leukaemia had better age-standardised survival (from 43% in Ecuador to ≥80% in parts of Europe, North America, Oceania, and Asia) than those with acute myeloid leukaemia (from 32% in Peru to ≥70% in most high-income countries in Europe, North America, and Oceania). Throughout 2000-14, survival from all leukaemias combined remained consistently higher for children than adolescents and young adults, and minimal improvement was seen for adolescents and young adults in most countries. INTERPRETATION: This study offers the first worldwide picture of population-based survival from leukaemia in children, adolescents, and young adults. Adolescents and young adults diagnosed with leukaemia continue to have lower survival than children. Trends in survival from leukaemia for adolescents and young adults are important indicators of the quality of cancer management in this age group. FUNDING: Children with Cancer UK, the Institut National du Cancer, La Ligue Contre le Cancer, Centers for Disease Control and Prevention, Swiss Re, Swiss Cancer Research foundation, Swiss Cancer League, Rossy Family Foundation, US National Cancer Institute, and the American Cancer Society.

Fetched live from OpenAlex and de-inverted. Abstracts are not stored in this database: the inverted indexes are 8.6 GB of the frame’s 9.3 GB of text, and the host has 13 GB free.

How this classification was reachedexpand

Full frame machine prediction

Teacher imitation

Not calibrated prevalence, not ground truth. Human validation pending. The Gemma side is a direct model label for every work in the frame, read from the title-only record. The Codex side is a classifier learned from the 10,348 direct Codex labels and calibrated to design-weighted sample rates; fields without enough sample support carry no Codex call. Candidate is the union of the two sides; consensus is their intersection. These outputs are machine_predicted_unvalidated and are not human labels.

metaresearch head score (Codex)0.003
metaresearch head score (Gemma)0.005
Version: metacan-v3-hybrid-931329e0061cValidation status: machine_predicted_unvalidated
Candidate categoriesnone
Consensus categoriesnone
DomainCandidate signal: none · Consensus signal: none
Study designCandidate signal: Observational · Consensus signal: Observational
GenreCandidate signal: Empirical · Consensus signal: Empirical
Teacher disagreement score0.071
Threshold uncertainty score0.140

Distilled classifier scores by category (both heads)

CategoryCodexGemma
Metaresearch0.0030.005
Meta-epidemiology (narrow)0.0000.000
Meta-epidemiology (broad)0.0010.001
Bibliometrics0.0030.007
Science and technology studies0.0000.000
Scholarly communication0.0010.001
Open science0.0010.001
Research integrity0.0010.001
Insufficient payload (model declined to judge)0.0010.000

Machine scores (provisional)

The two teacher heads of the student model, read on this work. A score orders the frame for review; it never asserts a category, and the validation status ships verbatim with every row.

Baseline scores from an immature model (maturity gate not passed, 7 training rounds). Scores rank; they never assert a category.

Opus teacher head0.027
GPT teacher head0.313
Teacher spread0.286 · how far apart the two teachers sit on this one work
Validation statusscore_only:v0-immature-baseline · verbatim from the scoring run: score_only means the number may rank works, and no category label ships from it

Classification

machine, unvalidated

Machine predicted; a candidate call from one source (direct Gemma or distilled Codex), not a consensus.

The models applied no category: nothing in the taxonomy fit this work.
Study designObservational
Domainnot available
GenreEmpirical

How this classification was reached, model by model and score by score, is at the end of the page under "How this classification was reached".

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Citations67
Published2022
Admission routes3
Has abstractyes

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Same venueThe Lancet Child & Adolescent HealthSame topicAcute Lymphoblastic Leukemia researchFrench-language works237,207