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Record W4308839581 · doi:10.1101/2022.11.08.22280168

Large-scale Rare Variant Burden Testing in Parkinson’s Disease Identifies Novel Associations with Genes Involved in Neuro-inflammation

2022· preprint· en· W4308839581 on OpenAlexaff
Mary B. Makarious, Julie Lake, Vanessa Pitz, Allen Ye Fu, Joseph L. Guidubaldi, Caroline Warly Solsberg, Sara Bandrés‐Ciga, Hampton L. Leonard, Jonggeol Jeffrey Kim, Kimberley J. Billingsley, Francis P. Grenn, Pilar Álvarez Jerez, Chelsea X. Alvarado, Hirotaka Iwaki, Michael Ta, Dan Vitale, Dena Hernández, Ali Torkamani, Mina Ryten, John Hardy, Sonja W. Scholz, Bryan J. Traynor, Clifton L. Dalgard, Debra Ehrlich, Toshiko Tanaka, Luigi Ferrucci, Thomas G. Beach, Geidy E. Serrano, Raquel Real, Huw R. Morris, Jinhui Ding, J. Raphael Gibbs, Andrew Singleton, Mike A. Nalls, Tushar Bhangale, Cornelis Blauwendraat

Bibliographic record

VenuemedRxiv · 2022
Typepreprint
Languageen
FieldMedicine
TopicParkinson's Disease Mechanisms and Treatments
Canadian institutionsCentre for Movement Disorders
FundersMedical Research Council
KeywordsLRRK2Parkinson's diseaseBiobankDiseaseExome sequencingTREM2ExomeGenome-wide association studyGenetic associationBiologyGeneticsGlucocerebrosidaseGeneBioinformaticsMedicineSingle-nucleotide polymorphismMutationGenotypeInternal medicine

Abstract

fetched live from OpenAlex

Abstract Parkinson’s disease (PD) has a large heritable component and genome-wide association studies to date have identified over 90 variants associated with PD, providing deeper insights into the disease biology. However, there have not been large-scale rare variant analyses for PD. To address this gap, we investigated the rare genetic component of PD at minor allele frequencies <1%, using whole genome and whole exome sequencing data from 7,184 PD cases, 6,701 proxy-cases, and 51,650 healthy controls from the Accelerating Medicines Partnership Parkinson’s disease (AMP-PD) initiative, the National Institutes of Health, the UK Biobank, and Genentech. We performed burden tests meta-analyses on protein-altering variants, prioritized based on their predicted functional impact. Our work identified several genes reaching exome-wide significance. While two of these genes, GBA and LRRK2 , have been previously implicated as risk factors for PD, we identify potential novel associations for B3GNT3, AUNIP, ADH5, TUBA1B, OR1G1, CAPN10 , and TREML1 . Of these, B3GNT3 and TREML1 provide new evidence for the role of neuroinflammation in PD. To date, this is the largest analysis of rare genetic variation in PD.

Fetched live from OpenAlex and de-inverted. Abstracts are not stored in this database: the inverted indexes are 8.6 GB of the frame’s 9.3 GB of text, and the host has 13 GB free.

How this classification was reachedexpand

Full frame machine prediction

Teacher imitation

Not calibrated prevalence, not ground truth. Human validation pending. The Gemma side is a direct model label for every work in the frame, read from the title-only record. The Codex side is a classifier learned from the 10,348 direct Codex labels and calibrated to design-weighted sample rates; fields without enough sample support carry no Codex call. Candidate is the union of the two sides; consensus is their intersection. These outputs are machine_predicted_unvalidated and are not human labels.

metaresearch head score (Codex)0.009
metaresearch head score (Gemma)0.011
Version: metacan-v3-hybrid-931329e0061cValidation status: machine_predicted_unvalidated
Candidate categoriesnone
Consensus categoriesnone
DomainCandidate signal: none · Consensus signal: none
Study designCandidate signal: Observational · Consensus signal: Observational
GenreCandidate signal: Empirical · Consensus signal: Empirical
Teacher disagreement score0.009
Threshold uncertainty score0.046

Distilled classifier scores by category (both heads)

CategoryCodexGemma
Metaresearch0.0090.011
Meta-epidemiology (narrow)0.0010.000
Meta-epidemiology (broad)0.0020.006
Bibliometrics0.0020.002
Science and technology studies0.0010.000
Scholarly communication0.0020.001
Open science0.0010.001
Research integrity0.0010.001
Insufficient payload (model declined to judge)0.0040.000

Machine scores (provisional)

The two teacher heads of the student model, read on this work. A score orders the frame for review; it never asserts a category, and the validation status ships verbatim with every row.

Baseline scores from an immature model (maturity gate not passed, 7 training rounds). Scores rank; they never assert a category.

Opus teacher head0.033
GPT teacher head0.268
Teacher spread0.235 · how far apart the two teachers sit on this one work
Validation statusscore_only:v0-immature-baseline · verbatim from the scoring run: score_only means the number may rank works, and no category label ships from it

Classification

machine, unvalidated

Machine predicted; a candidate call from one source (direct Gemma or distilled Codex), not a consensus.

The models applied no category: nothing in the taxonomy fit this work.
Study designObservational
Domainnot available
GenreEmpirical

How this classification was reached, model by model and score by score, is at the end of the page under "How this classification was reached".

Quick stats

Citations5
Published2022
Admission routes1
Has abstractyes

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