Bibliographic record
Abstract
The Canadian Porphyria Foundation (CPF) had its beginning in the mind of a person who had experienced the lack of knowledge and support when searching for porphyria information in the mid-1970s.In January 1988, a group of six volunteers armed with $350 set out on a mission "to improve the quality of life for people affected by porphyria".The Canadian Porphyria Foundation was formed by September 1988 with the national office located in Neepawa, Manitoba.The CPF is the only organization of its kind in Canada and is dedicated to providing quality service and support to porphyria sufferers not only in Canada, but globally as well.Since its inception 17 years ago, the CPF has come a long way.It has progressed from being a small rural organization into an international resource of information for porphyric patients.Recently, the CPF had its educational guides printed bilingually and will soon have its "Porphyria Safe and Unsafe Drug Guide" updated and also printed bilingually.This year on June 1, National Porphyria Day was celebrated for the first time in Canadian medical history.Many people, even those in the medical field, have not heard of porphyria or don't know that it is a disease.Porphyria is not a single disease, but is a group of disorders of at least eight different types.It is the result of an accumulation of porphyrins in the body caused by an enzyme deficiency that occurs due to a genetic defect.Porphyrins are normal body chemicals that can be found in plants and animals.They are produced in the liver and bone marrow and are necessary in the production of heme, which goes on to make hemoglobin.Hemoglobin is the red blood cells that transport oxygen from the lungs to the tissues of the body.Porphyria is a hereditary disease, but also can be acquired after exposure to certain chemicals.Symptoms of porphyria may include extreme sun sensitivity, abdominal pain, nausea and vomiting, muscle pain and weakness, psychosis, hallucinations, seizures and limb and respiratory paralysis.In rare cases, it can result in death.
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How this classification was reachedexpand
Full frame machine prediction
Teacher imitationNot calibrated prevalence, not ground truth. Human validation pending. The Gemma side is a direct model label for every work in the frame, read from the title-only record. The Codex side is a classifier learned from the 10,348 direct Codex labels and calibrated to design-weighted sample rates; fields without enough sample support carry no Codex call. Candidate is the union of the two sides; consensus is their intersection. These outputs are machine_predicted_unvalidated and are not human labels.
Distilled classifier scores by category (both heads)
| Category | Codex | Gemma |
|---|---|---|
| Metaresearch | 0.001 | 0.002 |
| Meta-epidemiology (narrow) | 0.000 | 0.000 |
| Meta-epidemiology (broad) | 0.001 | 0.000 |
| Bibliometrics | 0.001 | 0.001 |
| Science and technology studies | 0.001 | 0.004 |
| Scholarly communication | 0.003 | 0.003 |
| Open science | 0.001 | 0.001 |
| Research integrity | 0.003 | 0.003 |
| Insufficient payload (model declined to judge) | 0.003 | 0.000 |
Machine scores (provisional)
The two teacher heads of the student model, read on this work. A score orders the frame for review; it never asserts a category, and the validation status ships verbatim with every row.
Baseline scores from an immature model (maturity gate not passed, 7 training rounds). Scores rank; they never assert a category.
score_only:v0-immature-baseline · verbatim from the scoring run: score_only means the number may rank works, and no category label ships from itClassification
machine, unvalidatedMachine predicted; a candidate call from one source (direct Gemma or distilled Codex), not a consensus.
How this classification was reached, model by model and score by score, is at the end of the page under "How this classification was reached".