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Record W4408300642 · doi:10.1016/j.jcf.2025.02.015

Application of the defect distribution index to functional lung MRI of pediatric cystic fibrosis lung disease and controls

2025· article· en· W4408300642 on OpenAlexafffund
Elisabeth Kieninger, Samal Munidasa, Marion Curdy, Carmen Streibel, Brandon Zanette, Jason C. Woods, Philipp Latzin, Félix Ratjen, Giles Santyr

Bibliographic record

VenueJournal of Cystic Fibrosis · 2025
Typearticle
Languageen
FieldPhysics and Astronomy
TopicAtomic and Subatomic Physics Research
Canadian institutionsUniversity of TorontoHospital for Sick Children
FundersNatural Sciences and Engineering Research Council of CanadaCanadian Institutes of Health ResearchHospital for Sick ChildrenSchweizerischer Nationalfonds zur Förderung der Wissenschaftlichen ForschungNational Science Foundation
KeywordsMedicineCystic fibrosisLungMagnetic resonance imagingLung diseaseVentilation (architecture)RadiologyNuclear medicineDistribution (mathematics)Internal medicineMathematics

Abstract

fetched live from OpenAlex

Introduction Functional magnetic resonance imaging (MRI) of the lung usually assesses lung impairment as ventilation defect percentage (VDP). However, VDP only reflects the overall burden of disease and does not characterize the regional distribution (i.e. pattern) of defects. The defect distribution index (DDI) is a metric which shows quantitatively how clustered versus scattered defects are with a higher DDI indicating more clustered defects. Aim To assess the applicability and validity of the DDI to 129 Xe-MRI and PREFUL-MRI of CF lung disease. Methods The DDI algorithm was applied to fractional ventilation maps previously acquired with 129 Xe-MRI and PREFUL-MRI of 37 children with CF and 13 healthy controls. Results The calculation of DDI was feasible for all MRI data. DDI was significantly higher in patients with CF compared to healthy controls (mean difference [95 % CI] 129 Xe-MRI DDI 60 %mean -1.94 [-2.86 – -1.02], p=0.0001), strongly correlated with other functional outcomes such as VDP and the lung clearance index, and decreased significantly in CF patients with pulmonary exacerbations after antibiotic treatment (e.g. 129 Xe-MRI DDI 60 % mean –1.03 [-0.44 – -1.63], p=0.002). Conclusion The DDI is applicable to functional 129 Xe-MRI and PREFUL-MRI data providing complementary information to VDP by assessing defect distribution rather than defect size. It shows meaningful clinimetric properties and improves with treatment. The DDI shows potential as a parameter for comprehensive monitoring of CF lung disease and treatment.

Fetched live from OpenAlex and de-inverted. Abstracts are not stored in this database: the inverted indexes are 8.6 GB of the frame’s 9.3 GB of text, and the host has 13 GB free.

How this classification was reachedexpand

Full frame distilled prediction

Teacher imitation

Not calibrated prevalence, not ground truth. Human validation pending. Learned from the 10,348 direct Codex labels and 10,348 direct Gemma labels. Candidate is the union of thresholded teacher heads; consensus is their intersection. These outputs are machine_predicted_unvalidated and are not human labels or direct frontier model labels.

metaresearch head score (Codex)0.000
metaresearch head score (Gemma)0.000
Version: codex-gemma-dda1882f352aValidation status: machine_predicted_unvalidated
Candidate categoriesnone
Consensus categoriesnone
DomainCandidate signal: none · Consensus signal: none
Study designCandidate signal: Observational · Consensus signal: Observational
GenreCandidate signal: Empirical · Consensus signal: none
Teacher disagreement score0.580
Threshold uncertainty score0.379

Codex and Gemma teacher scores by category

CategoryCodexGemma
Metaresearch0.0000.000
Meta-epidemiology (narrow)0.0000.000
Meta-epidemiology (broad)0.0000.000
Bibliometrics0.0000.000
Science and technology studies0.0000.000
Scholarly communication0.0000.000
Open science0.0000.000
Research integrity0.0000.000
Insufficient payload (model declined to judge)0.0000.000

Machine scores (provisional)

The two teacher heads of the student model, read on this work. A score orders the frame for review; it never asserts a category, and the validation status ships verbatim with every row.

Baseline scores from an immature model (maturity gate not passed, 7 training rounds). Scores rank; they never assert a category.

Opus teacher head0.005
GPT teacher head0.252
Teacher spread0.247 · how far apart the two teachers sit on this one work
Validation statusscore_only:v0-immature-baseline · verbatim from the scoring run: score_only means the number may rank works, and no category label ships from it

Classification

machine, unvalidated

Machine predicted; a candidate call from one teacher head, not a consensus.

The models applied no category: nothing in the taxonomy fit this work.
Study designObservational
Domainnot available
GenreEmpirical

How this classification was reached, model by model and score by score, is at the end of the page under "How this classification was reached".

Quick stats

Citations1
Published2025
Admission routes2
Has abstractyes

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