MétaCan
Menu
Back to cohort
Record W1651380330

Empty Sella Syndrome: Report Of Two Siblings

2010· article· en· W1651380330 on OpenAlexvenueno aff
Janet Hong, Fuziah Mz, H Zaihawa

Bibliographic record

VenueJournal of Endocrinology and Metabolism · 2010
Typearticle
Languageen
FieldMedicine
TopicGrowth Hormone and Insulin-like Growth Factors
Canadian institutionsnot available
Fundersnot available
KeywordsMedicineShort statureEmpty sella syndromePediatricsSubclinical infectionBone ageGrowth hormone deficiencyDwarfismInternal medicineGrowth hormoneEndocrinologyHormone
DOInot available

Abstract

fetched live from OpenAlex

Introduction: About 10% of patients with combined pituitary hormones deficiencies (CPHD) have an affected first degree relative, which can be due to mutation of POU1F1 or PROP1 gene. We described 2 siblings with empty sella syndrome. Case Report: A 6 years 3 months old Chinese boy presented with short stature. He had poor growth since 1 year old but remained active and well. He had normal bowel and urinary habits. He has 2 elder sisters, aged 10 years and 8 years. Both parents are non consanguineous and are of normal height. He was not dysmorphic and had primary dentition. His body was proportionate with no skeletal deformity. His weight and height were below 3rd percentile, while head circumference was at 10th percentile. Systemic examination was normal. His growth velocity over a 9-month duration was 2.4 cm/year. He had iron deficiency anemia and was treated with iron supplement. Growth hormone (GH) provocative tests confirmed severe growth hormone deficiency. MRI pituitary in 2007 showed empty sella. GH replacement therapy was initiated at the age of 7 years. Six months later, he had subclinical hypothyroidism. His 8 year-old-sister was also short and later confirmed to have severe GH deficiency. However, she had a normal MRI pituitary. Conclusion: These 2 siblings have familial pituitary hormones deficiencies likely caused by mutation of either PROP1 or POU1F1 gene, which can be confirmed by genetic studies. Department of Paediatrics, Hospital Putrajaya, Putrajaya, Malaysia

Fetched live from OpenAlex and de-inverted. Abstracts are not stored in this database: the inverted indexes are 8.6 GB of the frame’s 9.3 GB of text, and the host has 13 GB free.

How this classification was reachedexpand

Full frame machine prediction

Teacher imitation

Not calibrated prevalence, not ground truth. Human validation pending. The Gemma side is a direct model label for every work in the frame, read from the title-only record. The Codex side is a classifier learned from the 10,348 direct Codex labels and calibrated to design-weighted sample rates; fields without enough sample support carry no Codex call. Candidate is the union of the two sides; consensus is their intersection. These outputs are machine_predicted_unvalidated and are not human labels.

metaresearch head score (Codex)0.001
metaresearch head score (Gemma)0.003
Version: metacan-v3-hybrid-931329e0061cValidation status: machine_predicted_unvalidated
Candidate categoriesnone
Consensus categoriesnone
DomainCandidate signal: none · Consensus signal: none
Study designCandidate signal: Case report · Consensus signal: Case report
GenreCandidate signal: Empirical · Consensus signal: Empirical
Teacher disagreement score0.005
Threshold uncertainty score0.013

Distilled classifier scores by category (both heads)

CategoryCodexGemma
Metaresearch0.0010.003
Meta-epidemiology (narrow)0.0030.002
Meta-epidemiology (broad)0.0010.001
Bibliometrics0.0020.001
Science and technology studies0.0030.002
Scholarly communication0.0020.002
Open science0.0020.003
Research integrity0.0050.003
Insufficient payload (model declined to judge)0.0040.001

Machine scores (provisional)

The two teacher heads of the student model, read on this work. A score orders the frame for review; it never asserts a category, and the validation status ships verbatim with every row.

Baseline scores from an immature model (maturity gate not passed, 7 training rounds). Scores rank; they never assert a category.

Opus teacher head0.015
GPT teacher head0.288
Teacher spread0.273 · how far apart the two teachers sit on this one work
Validation statusscore_only:v0-immature-baseline · verbatim from the scoring run: score_only means the number may rank works, and no category label ships from it

Classification

machine, unvalidated

Machine predicted; a candidate call from one source (direct Gemma or distilled Codex), not a consensus.

The models applied no category: nothing in the taxonomy fit this work.
Study designCase report
Domainnot available
GenreEmpirical

How this classification was reached, model by model and score by score, is at the end of the page under "How this classification was reached".

Quick stats

Citations0
Published2010
Admission routes1
Has abstractyes

Explore more

Same venueJournal of Endocrinology and MetabolismSame topicGrowth Hormone and Insulin-like Growth FactorsFrench-language works237,207