MétaCan
Menu
Back to cohort

UNEXPECTED BENEFIT OF PROPOFOL IN STIFF-PERSON SYNDROME

2008· article· en· W2099840024 on OpenAlex
Erin Hattan, Mark Angle, Claudia Chalk

Why this work is in the frame

A frame that forgets how it found something cannot be audited. These are the routes that admitted this work.

affAt least one author lists a Canadian institution in the pinned OpenAlex snapshot.

Bibliographic record

VenueNeurology · 2008
Typearticle
Languageen
FieldMedicine
TopicAutoimmune Neurological Disorders and Treatments
Canadian institutionsMcGill University
Fundersnot available
KeywordsStiff person syndromeGlutamate decarboxylaseAutoantibodyMedicineGABAergicPathophysiologyAmphiphysinInhibitory postsynaptic potentialAntibodyImmunologyNeuroscienceMyasthenia gravisImmune systemInternal medicineReceptorBiology

Abstract

fetched live from OpenAlex

Stiff person syndrome (SPS) is a rare autoimmune disorder characterized by severely increased axial muscular tone with superimposed “progressive fluctuating muscular rigidity and spasms,” despite an otherwise normal neurologic examination.1 An association with autoimmune disease was noted early on, and in 1988 high titers of autoantibodies directed against glutamic acid decarboxylase (GAD) were found in patients with SPS.2 GAD catalyzes the rate-limiting step in the synthesis of gamma-aminobutyric acid (GABA), the principal inhibitory neurotransmitter of the CNS. These observations, along with the known beneficial effects of drugs that enhance GABAergic neurotransmission, underlie the current concept of SPS as an immune-mediated pathologic impairment of central inhibition. This concept is supported by various electrophysiologic studies.3 SPS has also been described as a paraneoplastic syndrome in association with several types of tumors, including breast and small cell lung cancer. Paraneoplastic SPS may be associated with anti-GAD antibodies, as well as amphiphysin 1, gephyrin, or Ri antibodies.4 Although the pathophysiology of non-paraneoplastic SPS is incompletely understood, effective treatments include immunomodulating therapies and drugs that enhance GABAergic neurotransmission. Unfortunately, these treatments may lose …

Fetched live from OpenAlex and de-inverted. Abstracts are not stored in this database: the inverted indexes are 8.6 GB of the frame’s 9.3 GB of text, and the host has 13 GB free.

Full frame distilled prediction

Teacher imitation

Not calibrated prevalence, not ground truth. Human validation pending. Learned from the 10,348 direct Codex labels and 10,348 direct Gemma labels. Candidate is the union of thresholded teacher heads; consensus is their intersection. These outputs are machine_predicted_unvalidated and are not human labels or direct frontier model labels.

metaresearch head score (Codex)0.000
metaresearch head score (Gemma)0.000
Version: codex-gemma-dda1882f352aValidation status: machine_predicted_unvalidated
Candidate categoriesnone
Consensus categoriesnone
DomainCandidate signal: none · Consensus signal: none
Study designCandidate signal: Observational · Consensus signal: Observational
GenreCandidate signal: Empirical · Consensus signal: Empirical
Teacher disagreement score0.013
Threshold uncertainty score0.389

Codex and Gemma teacher scores by category

CategoryCodexGemma
Metaresearch0.0000.000
Meta-epidemiology (narrow)0.0000.000
Meta-epidemiology (broad)0.0000.000
Bibliometrics0.0000.000
Science and technology studies0.0000.000
Scholarly communication0.0000.000
Open science0.0000.000
Research integrity0.0000.000
Insufficient payload (model declined to judge)0.0000.000

Machine scores (provisional)

The two teacher heads of the student model, read on this work. A score orders the frame for review; it never asserts a category, and the validation status ships verbatim with every row.

Baseline scores from an immature model (maturity gate not passed, 7 training rounds). Scores rank; they never assert a category.

Opus teacher head0.027
GPT teacher head0.244
Teacher spread0.216 · how far apart the two teachers sit on this one work
Validation statusscore_only:v0-immature-baseline · verbatim from the scoring run: score_only means the number may rank works, and no category label ships from it