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Record W3000501046 · doi:10.1212/wnl.0000000000009107

Disease modification and biomarker development in Parkinson disease

2020· review· en· W3000501046 on OpenAlexafffund
Alberto J. Espay, Lorraine V. Kalia, Ziv Gan‐Or, Caroline H. Williams‐Gray, Philippe L. Bédard, Steven M. Rowe, Francesca Morgante, Alfonso Fasano, Benjamin Stecher, Marcelo Kauffman, Matthew J. Farrer, Christopher S. Coffey, Michael A. Schwarzschild, Todd Sherer, Ronald B. Postuma, Antonio P. Strafella, Andrew Singleton, Roger A. Barker, Karl Kieburtz, C. Warren Olanow, Andrés M. Lozano, Jeffrey H. Kordower, Jesse M. Cedarbaum, Patrik Brundin, David G. Standaert, Anthony E. Lang

Bibliographic record

VenueNeurology · 2020
Typereview
Languageen
FieldMedicine
TopicParkinson's Disease Mechanisms and Treatments
Canadian institutionsToronto Western Hospital
FundersNational Heart, Lung, and Blood InstituteCanadian Glycomics NetworkNatural Sciences and Engineering Research Council of CanadaCanadian Institutes of Health ResearchAvid RadiopharmaceuticalsParkinsonfondenNational Institute of Diabetes and Digestive and Kidney DiseasesCollege of Engineering, Michigan State UniversityNational Institutes of HealthIpsenDystonia Medical Research Foundation CanadaMedical Research CouncilServierEMD SeronoEvelyn TrustJanssen PharmaceuticalsNovo NordiskUniversity of TorontoEdmond J. Safra Philanthropic FoundationIdorsia PharmaceuticalsH. Lundbeck A/SRosetrees TrustParkinson's UKParkinson CanadaAcademy of Medical SciencesDepartment of Health and Social CareNational Institute for Health and Care ResearchMersana TherapeuticsAustralian GovernmentUniversity of CambridgeUltragenyx PharmaceuticalPTC TherapeuticsAcorda TherapeuticsNational Center for Advancing Translational SciencesUS WorldMedsQuébec Consortium for Drug DiscoveryAllerganSarepta TherapeuticsConsejo Nacional de Investigaciones Científicas y TécnicasConsortium canadien en neurodégénérescence associée au vieillissementTarget ALSWeston Brain InstituteProthenaMichael J. Fox Foundation for Parkinson's ResearchJazz PharmaceuticalsVertex PharmaceuticalsWellcome TrustAmerican Academy of NeurologyFondation Brain CanadaOntario Brain InstituteMichigan State UniversityMcGill UniversityGenome British ColumbiaMayo Foundation for Medical Education and ResearchCHDI FoundationBristol-Myers SquibbTeva Pharmaceutical IndustriesNational Parkinson FoundationAxial BiotherapeuticsPfizerBiogenNational Institute of Neurological Disorders and StrokeChiesi FarmaceuticiSunovionYale UniversityAvanir PharmaceuticalsU.S. Department of DefenseUniversity of Alabama at BirminghamCanada First Research Excellence FundMassachusetts General HospitalUCB PharmaNational Space Biomedical Research InstituteUniversity of AlabamaNIHR Cambridge Biomedical Research CentreCystic Fibrosis FoundationEli Lilly and CompanyBuck Institute for Research on AgingSanofiMinistère de l'Économie, de la Science et de l'Innovation - QuébecAmerican Parkinson Disease AssociationGenentechAstraZenecaJohns Hopkins UniversityParkinson Society CanadaBoston Scientific CorporationGlaxoSmithKlineU.S. Department of Commerce
KeywordsDiseaseSynucleinopathiesBiomarkerClinical trialParkinson's diseaseAlpha-synucleinMedicineDrug trialNeuroscienceBioinformaticsPsychologyPathologyBiologyGenetics

Abstract

fetched live from OpenAlex

A fundamental question in advancing Parkinson disease (PD) research is whether it represents one disorder or many. Does each genetic PD inform a common pathobiology or represent a unique entity? Do the similarities between genetic and idiopathic forms of PD outweigh the differences? If aggregates of α-synuclein in Lewy bodies and Lewy neurites are present in most (α-synucleinopathies), are they also etiopathogenically significant in each (α-synuclein pathogenesis)? Does it matter that postmortem studies in PD have demonstrated that mixed protein-aggregate pathology is the rule and pure α-synucleinopathy the exception? Should we continue to pursue convergent biomarkers that are representative of the diverse whole of PD or subtype-specific, divergent biomarkers, present in some but absent in most? Have clinical trials that failed to demonstrate efficacy of putative disease-modifying interventions been true failures (shortcomings of the hypotheses, which should be rejected) or false failures (shortcomings of the trials; hypotheses should be preserved)? Each of these questions reflects a nosologic struggle between the lumper's clinicopathologic model that embraces heterogeneity of one disease and the splitter's focus on a pathobiology-specific set of diseases. Most important, even if PD is not a single disorder, can advances in biomarkers and disease modification be revised to concentrate on pathologic commonalities in large, clinically defined populations? Or should our efforts be reconstructed to focus on smaller subgroups of patients, distinguished by well-defined molecular characteristics, regardless of their phenotypic classification? Will our clinical trial constructs be revised to target larger and earlier, possibly even prodromal, cohorts? Or should our trials efforts be reconstructed to target smaller but molecularly defined presymptomatic or postsymptomatic cohorts? At the Krembil Knowledge Gaps in Parkinson's Disease Symposium, the tentative answers to these questions were discussed, informed by the failures and successes of the fields of breast cancer and cystic fibrosis.

Fetched live from OpenAlex and de-inverted. Abstracts are not stored in this database: the inverted indexes are 8.6 GB of the frame’s 9.3 GB of text, and the host has 13 GB free.

How this classification was reachedexpand

Full frame distilled prediction

Teacher imitation

Not calibrated prevalence, not ground truth. Human validation pending. Learned from the 10,348 direct Codex labels and 10,348 direct Gemma labels. Candidate is the union of thresholded teacher heads; consensus is their intersection. These outputs are machine_predicted_unvalidated and are not human labels or direct frontier model labels.

metaresearch head score (Codex)0.000
metaresearch head score (Gemma)0.000
Version: codex-gemma-dda1882f352aValidation status: machine_predicted_unvalidated
Candidate categoriesMeta-epidemiology (narrow)
Consensus categoriesnone
DomainCandidate signal: none · Consensus signal: none
Study designCandidate signal: Other design · Consensus signal: none
GenreCandidate signal: Review · Consensus signal: Review
Teacher disagreement score0.987
Threshold uncertainty score1.000

Codex and Gemma teacher scores by category

CategoryCodexGemma
Metaresearch0.0000.000
Meta-epidemiology (narrow)0.0000.000
Meta-epidemiology (broad)0.0010.000
Bibliometrics0.0000.000
Science and technology studies0.0000.000
Scholarly communication0.0000.000
Open science0.0000.000
Research integrity0.0000.000
Insufficient payload (model declined to judge)0.0000.000

Machine scores (provisional)

The two teacher heads of the student model, read on this work. A score orders the frame for review; it never asserts a category, and the validation status ships verbatim with every row.

Baseline scores from an immature model (maturity gate not passed, 7 training rounds). Scores rank; they never assert a category.

Opus teacher head0.067
GPT teacher head0.328
Teacher spread0.260 · how far apart the two teachers sit on this one work
Validation statusscore_only:v0-immature-baseline · verbatim from the scoring run: score_only means the number may rank works, and no category label ships from it

Classification

machine, unvalidated

Machine predicted; a candidate call from one teacher head, not a consensus.

Study designOther design
Domainnot available
GenreReview

How this classification was reached, model by model and score by score, is at the end of the page under "How this classification was reached".

Quick stats

Citations134
Published2020
Admission routes2
Has abstractyes

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