MétaCan
Menu
Back to cohort
Record W3122646042 · doi:10.1242/jcs.244012

The p.E152K-STIM1 mutation deregulates Ca2+ signaling contributing to chronic pancreatitis

2021· article· en· W3122646042 on OpenAlexafffund
Miguel Burgos, R. Philippe, Fabrice Antigny, Paul Buscaglia, Emmanuelle Masson, Sreya Mukherjee, P Dubar, Cédric Le Maréchal, Florence Campeotto, Nicolas Lebonvallet, Maud Frieden, Juan Llopis, Beatriz Domingo, Peter B. Stathopulos, Mitsuhiko Ikura, Wesley H. Brooks, Wayne C. Guida, Jian‐Min Chen, Claude Férec, Thierry Capiod, Olivier Mignen

Bibliographic record

VenueJournal of Cell Science · 2021
Typearticle
Languageen
FieldNeuroscience
TopicIon Channels and Receptors
Canadian institutionsPrincess Margaret Cancer CentreUniversity of TorontoUniversity Health NetworkWestern University
FundersMinisterio de Economía y CompetitividadSchweizerischer Nationalfonds zur Förderung der Wissenschaftlichen ForschungInstitut National de la Santé et de la Recherche MédicaleCanadian Institutes of Health ResearchNatural Sciences and Engineering Research Council of CanadaAlliance Nationale pour les Sciences de la Vie et de la Santé
KeywordsEndoplasmic reticulumSERCABiologySTIM1Cell biologyIntracellularCalcium signalingCrosstalkHEK 293 cellsPancreatitisSignal transductionEndocrinologyInternal medicineATPaseBiochemistryReceptorEnzymeMedicine

Abstract

fetched live from OpenAlex

ABSTRACT Since deregulation of intracellular Ca2+ can lead to intracellular trypsin activation, and stromal interaction molecule-1 (STIM1) protein is the main regulator of Ca2+ homeostasis in pancreatic acinar cells, we explored the Ca2+ signaling in 37 STIM1 variants found in three pancreatitis patient cohorts. Extensive functional analysis of one particular variant, p.E152K, identified in three patients, provided a plausible link between dysregulated Ca2+ signaling within pancreatic acinar cells and chronic pancreatitis susceptibility. Specifically, p.E152K, located within the STIM1 EF-hand and sterile α-motif domain, increased the release of Ca2+ from the endoplasmic reticulum in patient-derived fibroblasts and transfected HEK293T cells. This event was mediated by altered STIM1–sarco/endoplasmic reticulum calcium transport ATPase (SERCA) conformational change and enhanced SERCA pump activity leading to increased store-operated Ca2+ entry (SOCE). In pancreatic AR42J cells expressing the p.E152K variant, Ca2+ signaling perturbations correlated with defects in trypsin activation and secretion, and increased cytotoxicity after cholecystokinin stimulation. This article has an associated First Person interview with the first author of the paper.

Fetched live from OpenAlex and de-inverted. Abstracts are not stored in this database: the inverted indexes are 8.6 GB of the frame’s 9.3 GB of text, and the host has 13 GB free.

How this classification was reachedexpand

Full frame distilled prediction

Teacher imitation

Not calibrated prevalence, not ground truth. Human validation pending. Learned from the 10,348 direct Codex labels and 10,348 direct Gemma labels. Candidate is the union of thresholded teacher heads; consensus is their intersection. These outputs are machine_predicted_unvalidated and are not human labels or direct frontier model labels.

metaresearch head score (Codex)0.002
metaresearch head score (Gemma)0.002
Version: codex-gemma-dda1882f352aValidation status: machine_predicted_unvalidated
Candidate categoriesnone
Consensus categoriesnone
DomainCandidate signal: none · Consensus signal: none
Study designCandidate signal: Bench or experimental · Consensus signal: Bench or experimental
GenreCandidate signal: Empirical · Consensus signal: Empirical
Teacher disagreement score0.006
Threshold uncertainty score0.865

Codex and Gemma teacher scores by category

CategoryCodexGemma
Metaresearch0.0020.002
Meta-epidemiology (narrow)0.0000.000
Meta-epidemiology (broad)0.0000.000
Bibliometrics0.0000.001
Science and technology studies0.0010.000
Scholarly communication0.0000.000
Open science0.0000.000
Research integrity0.0000.000
Insufficient payload (model declined to judge)0.0000.000

Machine scores (provisional)

The two teacher heads of the student model, read on this work. A score orders the frame for review; it never asserts a category, and the validation status ships verbatim with every row.

Baseline scores from an immature model (maturity gate not passed, 7 training rounds). Scores rank; they never assert a category.

Opus teacher head0.014
GPT teacher head0.263
Teacher spread0.249 · how far apart the two teachers sit on this one work
Validation statusscore_only:v0-immature-baseline · verbatim from the scoring run: score_only means the number may rank works, and no category label ships from it

Classification

machine, unvalidated

Machine predicted; a candidate call from one teacher head, not a consensus.

The models applied no category: nothing in the taxonomy fit this work.
Study designBench or experimental
Domainnot available
GenreEmpirical

How this classification was reached, model by model and score by score, is at the end of the page under "How this classification was reached".

Quick stats

Citations5
Published2021
Admission routes2
Has abstractyes

Explore more

Same venueJournal of Cell ScienceSame topicIon Channels and ReceptorsFrench-language works237,207