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Record W4400133061 · doi:10.52768/2379-1039/2209

Novel MYT1L gene mutation and cerebral palsy: A case report

2024· article· en· W4400133061 on OpenAlexaff
Johanie Victoria Piché, Myriam Srour, Michael Shevell

Bibliographic record

VenueOpen Journal of Clinical and Medical Case Reports · 2024
Typearticle
Languageen
FieldMedicine
TopicCerebral Palsy and Movement Disorders
Canadian institutionsMcGill UniversityMcGill University Health Centre
Fundersnot available
KeywordsCerebral palsyMicrocephalyMedicineMagnetic resonance imagingSpastic cerebral palsyEtiologyPediatricsPathologyPhysical medicine and rehabilitationSpasticRadiology

Abstract

fetched live from OpenAlex

Over the last decade, a body of genes that may underlie cerebral palsy causation has been elaborated. The objective of this case report is to highlight the possible implication of a loss-of-function pathogenic variant in myelin transcription factor-1 like (MYT1L) gene, not associated with cerebral palsy in prior literature, in the development of cerebral palsy. Our patient is a 22-month-old female referred for specialty evaluation of developmental delay who was subsequently diagnosed with spastic quadriplegic cerebral palsy. Normal magnetic resonance imaging and the finding of microcephaly prompted genetic analysis, which revealed a MYT1L pathogenic variant. Based on the critical function of MYT1L in brain development and based on the reported phenotypes associated with MYT1L, we conclude that a MYT1L pathogenic variant could contribute to the development of cerebral palsy. We therefore recommend that in cases of cerebral palsy where no acquired causes are identified and where, despite neurological findings beyond cerebral palsy (i.e., microcephaly), magnetic resonance imaging is normal, a genetic etiology should be suspected. In these cases, genetic testing should include testing specifically for the MYT1L gene as well as the other genes known to be associated with cerebral palsy.

Fetched live from OpenAlex and de-inverted. Abstracts are not stored in this database: the inverted indexes are 8.6 GB of the frame’s 9.3 GB of text, and the host has 13 GB free.

How this classification was reachedexpand

Full frame machine prediction

Teacher imitation

Not calibrated prevalence, not ground truth. Human validation pending. The Gemma side is a direct model label for every work in the frame, read from the title-only record. The Codex side is a classifier learned from the 10,348 direct Codex labels and calibrated to design-weighted sample rates; fields without enough sample support carry no Codex call. Candidate is the union of the two sides; consensus is their intersection. These outputs are machine_predicted_unvalidated and are not human labels.

metaresearch head score (Codex)0.001
metaresearch head score (Gemma)0.004
Version: metacan-v3-hybrid-931329e0061cValidation status: machine_predicted_unvalidated
Candidate categoriesnone
Consensus categoriesnone
DomainCandidate signal: none · Consensus signal: none
Study designCandidate signal: Case report · Consensus signal: Case report
GenreCandidate signal: Empirical · Consensus signal: Empirical
Teacher disagreement score0.010
Threshold uncertainty score0.018

Distilled classifier scores by category (both heads)

CategoryCodexGemma
Metaresearch0.0010.004
Meta-epidemiology (narrow)0.0030.002
Meta-epidemiology (broad)0.0020.002
Bibliometrics0.0050.003
Science and technology studies0.0050.004
Scholarly communication0.0030.004
Open science0.0030.004
Research integrity0.0100.006
Insufficient payload (model declined to judge)0.0040.001

Machine scores (provisional)

The two teacher heads of the student model, read on this work. A score orders the frame for review; it never asserts a category, and the validation status ships verbatim with every row.

Baseline scores from an immature model (maturity gate not passed, 7 training rounds). Scores rank; they never assert a category.

Opus teacher head0.070
GPT teacher head0.420
Teacher spread0.350 · how far apart the two teachers sit on this one work
Validation statusscore_only:v0-immature-baseline · verbatim from the scoring run: score_only means the number may rank works, and no category label ships from it

Classification

machine, unvalidated

Machine predicted; a candidate call from one source (direct Gemma or distilled Codex), not a consensus.

The models applied no category: nothing in the taxonomy fit this work.
Study designCase report
Domainnot available
GenreEmpirical

How this classification was reached, model by model and score by score, is at the end of the page under "How this classification was reached".

Quick stats

Citations0
Published2024
Admission routes1
Has abstractyes

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