MétaCan
Menu
← Back to cohort
Record W4402373844 · doi:10.1136/jnnp-2024-ehdn.326

J005 An update on select-hd, which is evaluating an allele-selective mutant huntingtin lowering approach in Huntington’s disease

2024· article· en· W4402373844 on OpenAlexaff
Asela Bandara, Oksana Suchowersky, Ralf Reilmann, Tiago Mestre, Joseph Haegele, Xiao Hu, Shushma Patel, Mark P. McLaughlin, N. Padma, Ty McClure, Varun Goel, Mark R. Hurtt, Michael Panzara, Jane Atkins, A. Li-Kwai-Cheung

Bibliographic record

Venuenot available
Typearticle
Languageen
FieldNeuroscience
TopicGenetic Neurodegenerative Diseases
Canadian institutionsUniversity of Alberta
Fundersnot available
KeywordsHuntingtinHuntington's diseaseAlleleMutantHuntingtin ProteinTrinucleotide repeat expansionDiseaseBiologyComputer scienceGeneticsGeneMedicineInternal medicine

Abstract

fetched live from OpenAlex

SELECT-HD is a phase 1b/2a clinical trial evaluating the investigational antisense oligonucleotide WVE-003 in early manifest Huntington’s disease. WVE-003 is designed to target a single nucleotide polymorphism (SNP3) that is associated with the mutant huntingtin allele (mHTT), enabling allele-selective lowering of mHTT and relative sparing of wild-type HTT (wtHTT). In September 2022, data from the first 18 participants who were administered a single dose of WVE-003 (30 mg, n=4; 60 mg, n=4; 90 mg, n=4; placebo, n=6) were reported. Through September 20, WVE-003 (30, 60, 90 mg) appeared generally safe and well-tolerated, with no serious adverse events or discontinuations. Adverse events were balanced across active and placebo groups, and mild-to-moderate in intensity. For biomarker analyses, the 30 and 60 mg cohorts were pooled, as only these cohorts had reached day 85, and there was no apparent dose response. The mean reduction in CSF mHTT compared with placebo was 35% (22% compared with baseline). Measured CSF wtHTT protein appeared consistent with allele-selectivity. Increases in neurofilament light chain from baseline were observed in some participants, and there were no clinically meaningful elevations in CSF white blood cell counts or protein that would indicate inflammation in the CNS. These data provided early indications of target engagement and a favorable safety profile for WVE-003 and enabled SELECT-HD to be adapted to expand the single-dose cohorts and to initiate a multidose cohort (30 mg dosed every eight weeks, n=24). This presentation will provide updated biomarker and safety data for all ongoing cohorts.

Fetched live from OpenAlex and de-inverted. Abstracts are not stored in this database: the inverted indexes are 8.6 GB of the frame’s 9.3 GB of text, and the host has 13 GB free.

How this classification was reachedexpand

Full frame machine prediction

Teacher imitation

Not calibrated prevalence, not ground truth. Human validation pending. The Gemma side is a direct model label for every work in the frame, read from the title-only record. The Codex side is a classifier learned from the 10,348 direct Codex labels and calibrated to design-weighted sample rates; fields without enough sample support carry no Codex call. Candidate is the union of the two sides; consensus is their intersection. These outputs are machine_predicted_unvalidated and are not human labels.

metaresearch head score (Codex)0.002
metaresearch head score (Gemma)0.004
Version: metacan-v3-hybrid-931329e0061cValidation status: machine_predicted_unvalidated
Candidate categoriesnone
Consensus categoriesnone
DomainCandidate signal: none · Consensus signal: none
Study designCandidate signal: Not applicable · Consensus signal: Not applicable
GenreCandidate signal: Other · Consensus signal: none
Teacher disagreement score0.013
Threshold uncertainty score0.043

Distilled classifier scores by category (both heads)

CategoryCodexGemma
Metaresearch0.0020.004
Meta-epidemiology (narrow)0.0010.001
Meta-epidemiology (broad)0.0020.002
Bibliometrics0.0020.002
Science and technology studies0.0010.000
Scholarly communication0.0030.002
Open science0.0020.001
Research integrity0.0030.004
Insufficient payload (model declined to judge)0.0130.006

Machine scores (provisional)

The two teacher heads of the student model, read on this work. A score orders the frame for review; it never asserts a category, and the validation status ships verbatim with every row.

Baseline scores from an immature model (maturity gate not passed, 7 training rounds). Scores rank; they never assert a category.

Opus teacher head0.046
GPT teacher head0.329
Teacher spread0.283 · how far apart the two teachers sit on this one work
Validation statusscore_only:v0-immature-baseline · verbatim from the scoring run: score_only means the number may rank works, and no category label ships from it

Classification

machine, unvalidated

Machine predicted; a candidate call from one source (direct Gemma or distilled Codex), not a consensus.

The models applied no category: nothing in the taxonomy fit this work.
Study designNot applicable
Domainnot available
GenreOther

How this classification was reached, model by model and score by score, is at the end of the page under "How this classification was reached".

Quick stats

Citations0
Published2024
Admission routes1
Has abstractyes

Explore more

Same topicGenetic Neurodegenerative Diseases→French-language works237,207→