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Record W4404871826 · doi:10.1016/j.xcrm.2024.101839

Endoplasmic reticulum stress-related deficits in calcium clearance promote neuronal dysfunction that is prevented by SERCA2 gene augmentation

2024· article· en· W4404871826 on OpenAlex
Yukihiro Shiga, Aline Giselle Rangel Olguin, Sana El Hajji, Nicolás Belforte, Heberto Quintero, Florence Dotigny, Luis Alarcón-Martínez, Arjun Krishnaswamy, Adriana Di Polo

Why this work is in the frame

A frame that forgets how it found something cannot be audited. These are the routes that admitted this work.

affAt least one author lists a Canadian institution in the pinned OpenAlex snapshot.
fundA Canadian funder is recorded on the work.

Bibliographic record

VenueCell Reports Medicine · 2024
Typearticle
Languageen
FieldBiochemistry, Genetics and Molecular Biology
TopicEndoplasmic Reticulum Stress and Disease
Canadian institutionsMcGill UniversityCentre Hospitalier de l’Université de Montréal
FundersAlcon Research InstituteFonds de Recherche du Québec - SantéUehara Memorial FoundationCanadian Institutes of Health ResearchNatural Sciences and Engineering Research Council of CanadaConsejo Nacional de Ciencia y TecnologíaCanada Excellence Research Chairs, Government of Canada
KeywordsEndoplasmic reticulumCalciumReticulumUnfolded protein responseMedicineGeneEndocrinologyInternal medicineNeurosciencePharmacologyCell biologyPsychologyBiologyGenetics

Abstract

fetched live from OpenAlex

Disruption of calcium (Ca 2+ ) homeostasis in neurons is a hallmark of neurodegenerative diseases. Here, we investigate the mechanisms leading to Ca 2+ dysregulation and ask whether altered Ca 2+ dynamics impinge on neuronal stress and circuit dysfunction. Using two-photon microscopy, we show that ocular hypertension, a major risk factor in glaucoma, and optic nerve crush injury disrupt the capacity of retinal neurons to clear cytosolic Ca 2+ leading to impaired light-evoked responses. Gene- and protein expression analysis reveal the loss of the sarco-endoplasmic reticulum (ER) Ca 2+ -ATPase2 pump (SERCA2/ ATP2A2 ) in injured retinal neurons from mice and patients with primary open-angle glaucoma. Pharmacological activation or neuron-specific gene delivery of SERCA2 is sufficient to rescue single-cell Ca 2+ dynamics and promote robust survival of damaged neurons. Furthermore, SERCA2 gene supplementation reduces ER stress, reestablishes circuit balance, and restores visual behaviors. Our findings reveal that enhancing the Ca 2+ clearance capacity of vulnerable neurons alleviates organelle stress and promotes neurorecovery. • Calcium (Ca 2+ ) clearance capacity is compromised in injured retinal neurons • Ocular hypertension induces SERCA2 downregulation and ER stress • Increased SERCA2 activity restores Ca 2+ homeostasis and mitigates ER stress • SERCA2 gene augmentation promotes neuronal survival and restores visual function Using two-photon microscopy, Shiga et al. show that impaired calcium clearance and ER stress are hallmarks of neuronal dysfunction in preclinical models of glaucoma and traumatic optic neuropathy. SERCA2 gene therapy restores calcium homeostasis, alleviates organelles stress, and promotes neurorecovery of vulnerable neurons.

Fetched live from OpenAlex and de-inverted. Abstracts are not stored in this database: the inverted indexes are 8.6 GB of the frame’s 9.3 GB of text, and the host has 13 GB free.

Full frame distilled prediction

Teacher imitation

Not calibrated prevalence, not ground truth. Human validation pending. Learned from the 10,348 direct Codex labels and 10,348 direct Gemma labels. Candidate is the union of thresholded teacher heads; consensus is their intersection. These outputs are machine_predicted_unvalidated and are not human labels or direct frontier model labels.

metaresearch head score (Codex)0.000
metaresearch head score (Gemma)0.000
Version: codex-gemma-dda1882f352aValidation status: machine_predicted_unvalidated
Candidate categoriesnone
Consensus categoriesnone
DomainCandidate signal: none · Consensus signal: none
Study designCandidate signal: Bench or experimental · Consensus signal: Bench or experimental
GenreCandidate signal: Empirical · Consensus signal: Empirical
Teacher disagreement score0.009
Threshold uncertainty score0.925

Codex and Gemma teacher scores by category

CategoryCodexGemma
Metaresearch0.0000.000
Meta-epidemiology (narrow)0.0000.000
Meta-epidemiology (broad)0.0000.000
Bibliometrics0.0000.000
Science and technology studies0.0000.000
Scholarly communication0.0000.000
Open science0.0000.000
Research integrity0.0000.000
Insufficient payload (model declined to judge)0.0000.000

Machine scores (provisional)

The two teacher heads of the student model, read on this work. A score orders the frame for review; it never asserts a category, and the validation status ships verbatim with every row.

Baseline scores from an immature model (maturity gate not passed, 7 training rounds). Scores rank; they never assert a category.

Opus teacher head0.008
GPT teacher head0.246
Teacher spread0.238 · how far apart the two teachers sit on this one work
Validation statusscore_only:v0-immature-baseline · verbatim from the scoring run: score_only means the number may rank works, and no category label ships from it