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Record W4409412042 · doi:10.1084/jem.20231467

Enhanced TLR7-dependent production of type I interferon by pDCs underlies pandemic chilblains

2025· article· en· W4409412042 on OpenAlexaff
Fanny Saidoune, Danyel Lee, Jérémy Di Domizio, Corentin Le Floc’h, Raphael Jenelten, Jérémie Le Pen, Vincent Bondet, Ana Joncic, Marie‐Anne Morren, Vivien Béziat, Shen‐Ying Zhang, Emmanuelle Jouanguy, Darragh Duffy, Charles M. Rice, Curdin Conrad, Jacques Fellay, Jean‐Laurent Casanova, Michel Gilliet, Ahmad Yatim

Bibliographic record

VenueThe Journal of Experimental Medicine · 2025
Typearticle
Languageen
FieldMedicine
TopicDermatological and COVID-19 studies
Canadian institutionsSickKids FoundationHospital for Sick Children
FundersNational Center for Advancing Translational SciencesNational Cancer InstituteNational Institutes of HealthEuropean Academy of Dermatology and VenereologyFondation pour la Recherche MédicaleUniversité Paris-SaclayNational Institute of Allergy and Infectious DiseasesFisher Center for Alzheimer's Research FoundationAgence Nationale de la RechercheEuropean CommissionCancer Research InstituteInstitut National Du CancerSCOR Corporate Foundation for ScienceMinistère de l'Enseignement supérieur, de la Recherche et de l'InnovationInstitut National de la Santé et de la Recherche MédicaleFondation du SouffleNational Science FoundationEuropean Molecular Biology OrganizationRockefeller UniversityMeyer FoundationUniversité de ParisThrasher Research FundFondation LeenaardsSt. Giles FoundationGeorge Mason UniversityCentre Hospitalier Universitaire VaudoisEuropean Society for ImmunodeficienciesSchlumberger FoundationSchweizerischer Nationalfonds zur Förderung der Wissenschaftlichen ForschungHoward Hughes Medical Institute
KeywordsTLR7ImmunologyPlasmacytoid dendritic cellInterferonContext (archaeology)TLR9VirologyVirusBiologyInnate immune systemMedicineToll-like receptorAntigenDendritic cellImmune systemGeneticsGene

Abstract

fetched live from OpenAlex

Outbreaks of chilblains were reported during the COVID-19 pandemic. Given the essential role of type I interferon (I-IFN) in protective immunity against SARS-CoV-2 and the association of chilblains with inherited type I interferonopathies, we hypothesized that excessive I-IFN responses to SARS-CoV-2 might underlie the occurrence of chilblains in this context. We identified a transient I-IFN signature in chilblain lesions, accompanied by an acral infiltration of activated plasmacytoid dendritic cells (pDCs). Patients with chilblains were otherwise asymptomatic or had mild disease without seroconversion. Their leukocytes produced abnormally high levels of I-IFN upon TLR7 stimulation with agonists or ssRNA viruses-particularly SARS-CoV-2-but not with DNA agonists of TLR9 or the dsDNA virus HSV-1. Moreover, the patients' pDCs displayed cell-intrinsic hyperresponsiveness to TLR7 stimulation regardless of TLR7 levels. Inherited TLR7 or I-IFN deficiency confers a predisposition to life-threatening COVID-19. Conversely, our findings suggest that enhanced TLR7 activity in predisposed individuals could confer innate, pDC-mediated, sterilizing immunity to SARS-CoV-2 infection, with I-IFN-driven chilblains as a trade-off.

Fetched live from OpenAlex and de-inverted. Abstracts are not stored in this database: the inverted indexes are 8.6 GB of the frame’s 9.3 GB of text, and the host has 13 GB free.

How this classification was reachedexpand

Full frame distilled prediction

Teacher imitation

Not calibrated prevalence, not ground truth. Human validation pending. Learned from the 10,348 direct Codex labels and 10,348 direct Gemma labels. Candidate is the union of thresholded teacher heads; consensus is their intersection. These outputs are machine_predicted_unvalidated and are not human labels or direct frontier model labels.

metaresearch head score (Codex)0.000
metaresearch head score (Gemma)0.000
Version: codex-gemma-dda1882f352aValidation status: machine_predicted_unvalidated
Candidate categoriesnone
Consensus categoriesnone
DomainCandidate signal: none · Consensus signal: none
Study designCandidate signal: Bench or experimental · Consensus signal: Bench or experimental
GenreCandidate signal: Empirical · Consensus signal: Empirical
Teacher disagreement score0.032
Threshold uncertainty score0.258

Codex and Gemma teacher scores by category

CategoryCodexGemma
Metaresearch0.0000.000
Meta-epidemiology (narrow)0.0000.000
Meta-epidemiology (broad)0.0000.000
Bibliometrics0.0000.000
Science and technology studies0.0000.000
Scholarly communication0.0000.000
Open science0.0000.000
Research integrity0.0000.000
Insufficient payload (model declined to judge)0.0000.000

Machine scores (provisional)

The two teacher heads of the student model, read on this work. A score orders the frame for review; it never asserts a category, and the validation status ships verbatim with every row.

Baseline scores from an immature model (maturity gate not passed, 7 training rounds). Scores rank; they never assert a category.

Opus teacher head0.030
GPT teacher head0.348
Teacher spread0.318 · how far apart the two teachers sit on this one work
Validation statusscore_only:v0-immature-baseline · verbatim from the scoring run: score_only means the number may rank works, and no category label ships from it

Classification

machine, unvalidated

Machine predicted; a candidate call from one teacher head, not a consensus.

The models applied no category: nothing in the taxonomy fit this work.
Study designBench or experimental
Domainnot available
GenreEmpirical

How this classification was reached, model by model and score by score, is at the end of the page under "How this classification was reached".

Quick stats

Citations8
Published2025
Admission routes1
Has abstractyes

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