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Record W4416140595 · doi:10.1002/pbc.32163

Taking Care of the Caregivers: A Quality‐of‐Life Measure for the Parents of Children With Transfusion‐Dependent Thalassemia

2025· article· en· W4416140595 on OpenAlexaff
Robert J. Klaassen, Rania S. Khelifi, Nicholas Barrowman, Manuela Merelles‐Pulcini, Elliott Vichinsky, Melanie Kirby‐Allen, Ellis J. Neufeld, Janet L. Kwiatkowski, John K. Wu, Nancy L. Young

Bibliographic record

VenuePediatric Blood & Cancer · 2025
Typearticle
Languageen
FieldMedicine
TopicHemoglobinopathies and Related Disorders
Canadian institutionsBC Children's HospitalHospital for Sick ChildrenUniversity of OttawaChildren's Hospital of Eastern Ontario
Fundersnot available
KeywordsConstruct validityThalassemiaReliability (semiconductor)Measure (data warehouse)Construct (python library)DiseaseValidity

Abstract

fetched live from OpenAlex

BACKGROUND: Children with transfusion-dependent thalassemia (TDT), also known as thalassemia major, require monthly blood transfusions and regular iron chelation therapy for long-term survival. While the burden of caring for these children is recognized, little has been done to address the parents' experience. PROCEDURE: A 38-item parent self-report was included in the previously designed disease-specific tool, the transfusion-dependent quality-of-life questionnaire (TranQol), to identify the issues they may be facing. We wanted to ensure that the self-report was reliable and valid. Questionnaires were given to parents during their children's routine clinic visits as part of a multi-center North American study of the TranQol. Construct validity was assessed using Pearson's correlation with the Pediatric Quality of Life (PedsQL) Family Impact Module (FIM) (hypothesis: correlation of 0.4-0.6). RESULTS: Sixty-seven parents completed both the TranQol and PedsQL Family Impact Module questionnaires at baseline. There was substantial correlation (r = 0.76) between TranQol parent self-report scores (median 63, interquartile range [IQR]: 53-76) and PedsQL Family Impact Module scores (median 77, IQR: 59-89). CONCLUSIONS: The median PedsQL FIM score was similar to previously reported scores for parents of children with sickle cell disease. The TranQol parental burden tool demonstrated construct validity was internally reliable (Cronbach's α = 0.94) and had acceptable test-retest reliability (intraclass correlation coefficient [ICC] = 0.81), for future research into TDT. In addition, this tool could also be used to help clinicians assess the impact of the disease on parents to potentially target appropriate support and care that is required.

Fetched live from OpenAlex and de-inverted. Abstracts are not stored in this database: the inverted indexes are 8.6 GB of the frame’s 9.3 GB of text, and the host has 13 GB free.

How this classification was reachedexpand

Full frame machine prediction

Teacher imitation

Not calibrated prevalence, not ground truth. Human validation pending. The Gemma side is a direct model label for every work in the frame, read from the title-only record. The Codex side is a classifier learned from the 10,348 direct Codex labels and calibrated to design-weighted sample rates; fields without enough sample support carry no Codex call. Candidate is the union of the two sides; consensus is their intersection. These outputs are machine_predicted_unvalidated and are not human labels.

metaresearch head score (Codex)0.002
metaresearch head score (Gemma)0.007
Version: metacan-v3-hybrid-931329e0061cValidation status: machine_predicted_unvalidated
Candidate categoriesnone
Consensus categoriesnone
DomainCandidate signal: none · Consensus signal: none
Study designCandidate signal: Observational · Consensus signal: Observational
GenreCandidate signal: Empirical · Consensus signal: Empirical
Teacher disagreement score0.002
Threshold uncertainty score0.012

Distilled classifier scores by category (both heads)

CategoryCodexGemma
Metaresearch0.0020.007
Meta-epidemiology (narrow)0.0000.000
Meta-epidemiology (broad)0.0000.001
Bibliometrics0.0010.001
Science and technology studies0.0000.000
Scholarly communication0.0010.001
Open science0.0000.001
Research integrity0.0000.001
Insufficient payload (model declined to judge)0.0010.000

Machine scores (provisional)

The two teacher heads of the student model, read on this work. A score orders the frame for review; it never asserts a category, and the validation status ships verbatim with every row.

Baseline scores from an immature model (maturity gate not passed, 7 training rounds). Scores rank; they never assert a category.

Opus teacher head0.012
GPT teacher head0.272
Teacher spread0.260 · how far apart the two teachers sit on this one work
Validation statusscore_only:v0-immature-baseline · verbatim from the scoring run: score_only means the number may rank works, and no category label ships from it

Classification

machine, unvalidated

Machine predicted; a candidate call from one source (direct Gemma or distilled Codex), not a consensus.

The models applied no category: nothing in the taxonomy fit this work.
Study designObservational
Domainnot available
GenreEmpirical

How this classification was reached, model by model and score by score, is at the end of the page under "How this classification was reached".

Quick stats

Citations1
Published2025
Admission routes1
Has abstractyes

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